نتایج جستجو برای: synuclein

تعداد نتایج: 7040  

2008
Lokesh Kukreja Shubhik DebBurman

Parkinson’s disease is a progressive neurodegenerative disease caused by the death of midbrain dopaminergic neurons. The misfolding and aggregation of α-synuclein plays a ruinous role in this disease, but how the protein becomes toxic is unclear. Using yeasts as model organisms for studying α-synuclein properties, our study explores the hypothesis that α-synuclein toxicity depends on plasma mem...

Journal: :The Journal of clinical investigation 2015
Alevtina D Zharikov Jason R Cannon Victor Tapias Qing Bai Max P Horowitz Vipul Shah Amina El Ayadi Teresa G Hastings J Timothy Greenamyre Edward A Burton

Multiple convergent lines of evidence implicate both α-synuclein (encoded by SCNA) and mitochondrial dysfunction in the pathogenesis of sporadic Parkinson's disease (PD). Occupational exposure to the mitochondrial complex I inhibitor rotenone increases PD risk; rotenone-exposed rats show systemic mitochondrial defects but develop specific neuropathology, including α-synuclein aggregation and de...

2011
Thomas Näsström Susana Gonçalves Charlotte Sahlin Eva Nordström Valentina Screpanti Sundquist Lars Lannfelt Joakim Bergström Tiago F. Outeiro Martin Ingelsson

Recent research implicates soluble aggregated forms of α-synuclein as neurotoxic species with a central role in the pathogenesis of Parkinson's disease and related disorders. The pathway by which α-synuclein aggregates is believed to follow a step-wise pattern, in which dimers and smaller oligomers are initially formed. Here, we used H4 neuroglioma cells expressing α-synuclein fused to hemi:GFP...

2014
Yunchun Tai Ling Chen Enping Huang Chao Liu Xingyi Yang Pingming Qiu Huijun Wang

The over-expression of α-synuclein is a major factor in the death of dopaminergic neurons in a methamphetamine-induced model of Parkinson's disease. In the present study, α-synuclein knockdown rats were created by injecting α-synuclein-shRNA lentivirus stereotaxically into the right striatum of experimental rats. At 2 weeks post-injection, the rats were injected intraperitoneally with methamphe...

2010
Nandhakumar Thayanidhi Jared R. Helm Deborah C. Nycz Marvin Bentley Yingjian Liang Jesse C. Hay

Toxicity of human alpha-synuclein when expressed in simple organisms can be suppressed by overexpression of endoplasmic reticulum (ER)-to-Golgi transport machinery, suggesting that inhibition of constitutive secretion represents a fundamental cause of the toxicity. Whether similar inhibition in mammals represents a cause of familial Parkinson's disease has not been established. We tested elemen...

2016
Daniele Cartelli Alessandro Aliverti Alberto Barbiroli Carlo Santambrogio Enzio M. Ragg Francesca V.M. Casagrande Francesca Cantele Silvia Beltramone Jacopo Marangon Carmelita De Gregorio Vittorio Pandini Marco Emanuele Evelina Chieregatti Stefano Pieraccini Staffan Holmqvist Luigi Bubacco Laurent Roybon Gianni Pezzoli Rita Grandori Isabelle Arnal Graziella Cappelletti

α-Synuclein is a presynaptic protein associated to Parkinson's disease, which is unstructured when free in the cytoplasm and adopts α helical conformation when bound to vesicles. After decades of intense studies, α-Synuclein physiology is still difficult to clear up due to its interaction with multiple partners and its involvement in a pletora of neuronal functions. Here, we looked at the remar...

2015
Asuka Sasaki Shigeki Arawaka Hiroyasu Sato Takeo Kato

α-Synuclein deposited in Lewy bodies, a pathological hallmark of Parkinson's disease (PD), is highly phosphorylated at serine 129 (Ser129). In contrast, there is very little Ser129-phosphorylated α-synuclein in the normal brains. This difference suggests that Ser129-phosphorylation is involved in neurodegenerative processes of PD. However, the role of this modification remains unclear. One limi...

Journal: :Neuron 2013
Jacob T. Bendor Todd P. Logan Robert H. Edwards

Human genetics has indicated a causal role for the protein α-synuclein in the pathogenesis of familial Parkinson's disease (PD), and the aggregation of synuclein in essentially all patients with PD suggests a central role for this protein in the sporadic disorder. Indeed, the accumulation of misfolded α-synuclein now defines multiple forms of neural degeneration. Like many of the proteins that ...

2016
Ariadna Recasens Celine Perier Carolyn M. Sue

Growing evidence suggests that increased levels of α-synuclein might contribute to the pathogenesis of Parkinson's disease (PD) and therefore, it is crucial to understand the mechanisms underlying α-synuclein expression. Recently, microRNAs (miRNAs) have emerged as key regulators of gene expression involved in several diseases such as PD and other neurodegenerative disorders. A systematic liter...

2013
Theodore A. Sarafian Christopher M. Ryan Puneet Souda Eliezer Masliah Upendra K. Kar Harry V. Vinters Gary W. Mathern Kym F. Faull Julian P. Whitelegge Joseph B. Watson

While most forms of Parkinson's Disease (PD) are sporadic in nature, a small percentage of PD have genetic causes as first described for dominant, single base pair changes as well as duplication and triplication in the α-synuclein gene. The α-synuclein gene encodes a 140 amino acid residue protein that interacts with a variety of organelles including synaptic vesicles, lysosomes, endoplasmic re...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید