Absent pulmonic valve (APV) in tetralogy of Fallot produces a pulmonic regurgitation murmur (PRM) which is usually late in onset after A2, low pitched, and of crescendo-decrescendo character. We have seen three adult patients with tetralogy of Fallot with APV and have done intracardiac sound and pressure studies in two. The PRM was loudest in the RV outflow tract (RVOT), where the onset was ear...

BACKGROUND Public-health guidelines recommend patients with congenital heart disease to exercise. Studies have shown that patients with congenital heart disease can improve physical exercise capacity. The effect of training on regional ventricular performance has hardly been studied. We performed a pilot study to assess whether an exercise training program would result in adverse changes of reg...

Anomalous pulmonary venous connections were found in seven (0.6%) of 1183 patients with tetralogy of Fallot. Three patients had totally anomalous connections (one supracardiac, one direct to coronary sinus, and one mixed supracardiac and infracardiac) and four patients had partially anomalous pulmonary venous connections. All patients presented with the clinical features of tetralogy of Fallot....

OBJECTIVE To validate the accuracy of the prognostic significance of non-invasive clinical diagnostic indices as predictors of sustained ventricular tachycardia (sVT) or fibrillation (VF) in patients undergoing repair for tetralogy of Fallot. METHODS One way analysis of variance and pairwise comparison of the values with the Bonferroni correction, logistic multivariate analysis, and ordinal l...

Medical imaging plays a significant role in the detection of foetal anomalies, such as Pentalogy Cantrell (POC). POC is congenital anomaly involving five or fewer body malformations: ectopia cordis (EC), tetralogy fallot (TOF), sternal defects, diaphragmatic and abdominal wall defects. The commonly used modality during pregnancy ultrasound because it uses non-ionising radiation, cheap, availabl...

FALLOT'S tetralogy is a condition of cyanotic congenital heart disease associated with pulmonary stenosis and a ventricular septal defect. The right ventricular hypertrophy and overriding aorta are probably a result of the altered hemodynamics. The essential features of the condition are cyanosis, pulmonary stenosis and a ventricular septal defect. Consequently, the so-called Trilogy of Fallot ...

THE electrocardiogram in patients with tetralogy of Fallot usually shows right axis deviation and right ventricular hypertrophy. After creation of a systemic-pulmonary artery anastomosis, the work of the left ventricle increases, usually accompanied by a corresponding increase in the pattern of left ventricular loading." 2 Following openheart surgery, with closure of the ventricular septal defe...

Left ventricular function was assessed by angiographic methods in 40 patients (ages 3-27), 1-12 years following repair of tetralogy of Fallot. Twenty of the 40 patients (group A) had a satisfactory repair with a pulmonary-systemic flow ratio (Qp/Qs) less then or equal to 1.5 and a right ventricular systolic pressure of less than or equal to 60% of the left ventricular value. The other 20 patien...

The Tetralogy of Fallot is the most common cyanotic congénital heart disease. The regular form combines from four anomalies: A ventricular septal defect Pulmonary stenosis Overriding aorta A right ventricular hypertrophy. Irregular forms are all other forms where another heart defect is associated, among which are the anomalies of the coronary arteries found in 5-9% of cases that require specia...

T HE CLASSICAL subclavian-pulinonaryt and aortic-pulmonary2 anastomoses were devised as palliative surgical maneuvers for the tetralogy of Fallot complex to augment pulmonary blood flow and to increase systemic arterial saturation. These shunt procedures, performed during the past 14 years, have provided reasonably good health to thousands of patients with severe cyanosis and physical limitatio...