نتایج جستجو برای: von willebrand disease

تعداد نتایج: 1579959  

Journal: :Annals of the rheumatic diseases 1991
G Brevetti M De Caterina V D Martone S Corrado A Silvestro G Spadaro F Scopacasa

Adhesion molecules play a role in the inflammation and pathogenesis of vascular diseases. In 13 patients with primary Raynaud's phenomenon, 19 with Raynaud's phenomenon associated with connective tissue disease, and 16 control subjects, we measured plasma levels of soluble forms of intercellular adhesion molecule-1, vascular cell adhesion molecule-1, E-selectin, and von Willebrand factor. Patie...

Journal: :Blood 2008
Giancarlo Castaman Stefan Lethagen Augusto B Federici Alberto Tosetto Anne Goodeve Ulrich Budde Javier Batlle Dominique Meyer Claudine Mazurier Edith Fressinaud Jenny Goudemand Jeroen Eikenboom Reinhard Schneppenheim Jorgen Ingerslev Zdena Vorlova David Habart Lars Holmberg John Pasi Frank Hill Ian Peake Francesco Rodeghiero

We have prospectively evaluated the biologic response to desmopressin in 77 patients with type 1 von Willebrand disease (VWD) enrolled within the Molecular and Clinical Markers for the Diagnosis and Management of type 1 VWD project. Complete response to desmopressin was defined as an increase of both ristocetin cofactor activity (VWF:RCo) and factor VIII coagulant activity (FVIII:C) to 50 IU/dL...

Journal: :Thrombosis and haemostasis 2011
J Windyga M von Depka-Prondzinski

The aim of this study was to assess the efficacy of Wilate®, a new generation, plasma-derived, high-purity, double virus-inactivated von Willebrand factor (VWF) and factor VIII (FVIII) concentrate (ratio close to physiological 1:1) in the perioperative management of haemostasis in von Willebrand disease (VWD). Data for VWD patients who received Wilate® for perioperative management were obtained...

Journal: :Stroke 2010
Renske G Wieberdink Marianne C van Schie Peter J Koudstaal Albert Hofman Jacqueline C M Witteman Moniek P M de Maat Frank W G Leebeek Monique M B Breteler

BACKGROUND AND PURPOSE Many studies have investigated the role of plasma von Willebrand factor level in coronary heart disease, but few have investigated its role in stroke. The aim of this study was to determine if von Willebrand factor levels are associated with the risk of stroke. METHODS The study was part of the Rotterdam Study, a large population-based cohort study among subjects aged ≥...

Journal: :Best practice & research. Clinical haematology 2001
Z M Ruggeri

The adhesive protein von Willebrand factor mediates the initiation and progression of thrombus formation at sites of vascular injury. von Willebrand factor is synthesized in endothelial cells and megakaryocytes as a very large polymer composed of identical subunits. In the plasma, it appears as a series of multimers of regularly decreasing molecular mass, from several thousand to 500 kDa. The s...

2005
S. Coller

Two monoclonal antibodies-one that blocks ristocetininduced platelet binding of von Willebrand factor to glycoprotein lb and one that blocks adenosine diphosphateinduced binding of fibrinogen to the glycoprotein llb/Illa complex-were used to assess the binding site(s) for von Willebrand factor when platelets are stimulated with thrombin or adenosine diphosphate (ADP). Neither agonist induced bi...

Journal: :The Journal of clinical investigation 1976
C S Jenkins D R Phillips K J Clemetson D Meyer M J Larrieu E F Lüscher

The antibiotic ristocetin only aggregates platelets in the presence of plasma von Willebrand factor. Platelets from patients with Bernard-Soulier syndrome do not aggregate upon addition of ristocetin although, in contrast to von Willebrand's disease, plasma levels of factor VIII complex (factor VIII clotting activity, von Willebrand factor activity, and von Willebrand antigen) are normal. The m...

2010
Charlotte M Höög Olle Broström Tomas L Lindahl Andreas Hillarp Gerd Lärfars Urban Sjöqvist

BACKGROUND Angioectasias in the gastrointestinal tract can be found in up to 3% of the population. They are typically asymptomatic but may sometimes result in severe bleeding. The reasons for why some patients bleed from their angioectasias are not fully understood but it has been reported that it may be explained by an acquired von Willebrand syndrome (AVWS). This condition has similar laborat...

2016
K. E. Zlobina G. Th. Guria

Platelet activation in blood flow under high, overcritical shear rates is initiated by Von Willebrand factor. Despite the large amount of experimental data that have been obtained, the value of the critical shear rate, above which von Willebrand factor starts to activate platelets, is still controversial. Here, we recommend a theoretical approach to elucidate how the critical blood shear rate i...

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