In the past 25 years, major advances were achieved in the nosography of cardiomyopathies, influencing the definition and taxonomy of this important chapter of cardiovascular disease. Nearly, 50% of patients dying suddenly in childhood or adolescence or undergoing cardiac transplantation are affected by cardiomyopathies. Novel cardiomyopathies have been discovered (arrhythmogenic, restrictive, a...

Definition and Classification The cardiomyopathies are a diverse group of myocardial diseases that are characterized by chronic ventricular dysfunction. The clinical classification of cardiomyopathy is based on hemodynamic and echocardiographic abnormalities, and consists of dilated cardiomyopathy, hypertrophic cardiomyopathy, and restrictive cardiomyopathy. Recently, arrhythmogenic right ventr...

Cardiomyopathies are an important and heterogeneous group of diseases. The awareness and knowledge of these diseases in both the public and medical communities historically has been impaired by persistent confusion surrounding definitions and nomenclature. Classification schemes, of which there have been many, (Thiene et al., 2000, 2004; Richardson et al., 1996) are potentially useful in drawin...

Cardiomyopathies can generally be categorized into two groups, based on World Health Organization guidelines: extrinsic and intrinsic. In extrinsic cardiomyopathies the primary pathology is outside the myocardium. Most cardiomyopathies are extrinsic, because the most common cause is ischemia. Intrinsic cardiomyopathies is weakness in the muscle of the heart that is not due to an identifiable ex...

conclusions these findings emphasize the potential clinical benefits of therapeutic procedures such as cardiac resynchronization therapy (crt) or apex-sparing volume-reduction surgery in dcm. a better definition of the role and implications of reverse apical torsion in dcm and its importance and effectiveness in making therapeutic decisions like crt implantation requires further studies. case p...

The definition and classification of the cardiomyopathies has been traditionally a complex and quite variable subject. In 2006, the American Heart Association issued a scientific statement elaborated by a task force of experts that contemplated the important development of molecular genetics in recent years, to explain the etiology of the diseases of cardiac muscle, or cardiomyopathies, previou...

Cardiomyopathies constitute a heterogeneous group of diseases with varying etiologies and clinical presentation. Advances in genetic testing have made it possible to establish genotype-phenotype relationships, determine prognosis, choose specific treatments the pediatric population. Therefore, objective this review is assist reasoning underscore importance etiological diagnosis different diseas...