OBJECTIVE To report that maximum weakening of lateral rectus muscles can improve significant exotropia in primary position, abnormal head posture, retraction, narrowing of palpebral fissure and downshoot in exotropic duannes retraction syndrome. CASE A 12-year-old boy with exotropic Duane syndrome presented with downshoot and globe retraction in attempted adduction. Squint surgery was underta...

Case Age at Cause of No. Onset Sex Ophthalmoplegia Manifestation (yrs) 1 47 F S u b a r a c h no i d !Fuchs's phenomenon of lid retraction on adduction haemorrhage Pseudo-Graefe phenomenon of lid retraction on looking down 2 i F Typhoid Paradoxical retraction on occlusion of sound eye 3 5 M Head injury Lid retraction on attempted adduction Pseudo-Graefe phenomenon of lid retraction on looking d...

We report here a patient with type 1 Duane's retraction syndrome and multiple congenital abnormalities as a result of the VACTERL association. The presented combination of Duane's retraction syndrome and the VACTERL association has not been reported in the literature. The present case was instructive for reviewing the continuous spectrum of ocular anomalies that accompany the VACTERL association.

BACKGROUND Duane retraction syndrome (DRS) consists of abduction deficit, globe retraction and upshoots or downshoots with adduction. The abducens nerve on the affected side is absent in type 1 DRS. After bilateral medial rectus muscle recession in unilateral type 1 DRS may improve the abduction limitation, but still more than -3 limitation remains. CASE PRESENTATION A 6-month-old boy present...

In 1952, Wildervanck described the first case of what he styled the cervico-oculo-acoustic (COA) syndrome. This comprises Klippel Feil's (KF) anomaly (congenitally fused cervical vertebrae), congenital sensorineural deafness and Duane's retraction syndrome (deficient abduction with retraction on adduction). Since that original paper, there have been further reports describing this triad, either...

DUANE'S retraction syndrome (Duane, 1905) is frequently but not invariably associated with convergent strabismus when the eyes are in the primary position (Duke-Elder, 1964); if a head-turn is present, it will be in the direction of action of the paretic lateral rectus muscle. In the atypical retraction syndrome, the medial rectus is more paretic than the lateral rectus muscle; there is exophor...

1. Mohney BG, Huffaker RK. Common forms of childhood exotropia. Ophthalmology 2003;110:20936. 2. Duane TD, Schatz NJ, Caputo AR. Pseudo-Duane's retraction syndrome. Trans Am Ophthalmol Soc 1976;74:122-32. 3. Gittinger JW Jr, Hughes JP, Suran EL. Medial orbital wall blow-out fracture producing an acquired retraction syndrome. J Clin Neuroophthalmol 1986;6:153-6. 4. Gao Z, Guo H, Chen W. Initial ...

Duane (I905) emphasized six features of a characteristic congenital ocular motility syndrome: (i) Complete, or less often partial, loss of abduction of the affected eye; (2) Partial, or rarely complete, restriction of adduction of the aHected eye; (3) Retraction of the affected eye into the orbit on adduction; (4) Oblique overshoot of the affected eye either up and in or down and in on adductio...