Hamartomas are tumor-like lesions composed of tissue elements normally found at the site where they are located, but which grow in a disorganized manner. They generally occur at birth or soon after, although presentations during adult life have been reported. Hamartomas of the head and neck are very rare. The exact mechanisms behind the development of hamartomas remain unknown; however, their b...

Neurology India | May-Jun 2009 | Vol 57 | Issue 3 A 37-year-old gentleman presented with weakness, burning sensation, pain and a progressively increasing swelling in the volar aspect of the right palm and wrist for three years. On examination there was wasting of the thenar eminence with muscle power of MRC Grade II and decreased sensation in the median nerve distribution of the right hand. Ner...

http://www.sajr.org.za doi:10.4102/sajr.v19i2.886 Fibrolipomatous hamartoma is a rare benign tumour most commonly affecting the median nerve and is characterised by fibro-fatty nerve infiltration. It results in fusiform nerve enlargement with a pathognomonic ‘spaghetti-like’ imaging appearance. Patients present with numbness and paraesthesia and later with motor deficits in the affected nerve d...

macrodystrophia lipomatosa is a rare congenital form of localized gigantism characterized by an increase in all mesenchymal elements, particularly fibroadipose tissue. mr imaging can be used to examine the soft tissue and detect the fibrous and fatty hypertrophy that characterizes this condition and also diagnose an associated fibrolipomatous hamartoma of the median or plantar nerve. we describ...

Macrodystrophia lipomatosa is a rare congenital form of localized gigantism characterized by an increase in all mesenchymal elements, particularly fibroadipose tissue. MR imaging can be used to examine the soft tissue and detect the fibrous and fatty hypertrophy that characterizes this condition and also diagnose an associated fibrolipomatous hamartoma of the median or plantar nerve. We des...