Yaumatei Dermatology Clinic, 12/F, Yaumatei Specialist Clinic (New Extension), 143 Battery Street, Yaumatei, Kowloon, Hong Kong An eleven-month-old boy presented with increasing number of yellowish papules on scalp, trunk and limbs soon after birth. Skin biopsy revealed juvenile xanthogranuloma. He was also found to have multiple café-au-lait macules. The clinical course, complications and asso...

Systemic form of juvenile xanthogranuloma with involvement of liver and bone marrow is reported in a 2-month-old female infant who presented with hepatosplenomegaly, severe anemia, and thrombocytopenia. There was no skin lesion, nor bone lesion. The enlarged liver has generalized yellowish spots. The diagnosis of juvenile xanthogranuloma was made by pathologic findings of marrow and portal trac...

Juvenile xanthogranuloma is the most common form of non-Langerhans cell histiocytosis. It manifests clinically as a red-yellow papule, usually showing spontaneous remission. The diagnosis is based on clinical and histological findings. We report the use of dermoscopy (“setting sun” pattern) as an adjuvant tool in the diagnosis of juvenile xanthogranuloma in a female patient presenting with a 2-...

INTRODUCTION Orbital masses in adults are often caused by systemic diseases or are associated with systemic manifestations. Juvenile xanthogranuloma as a cause is rare and unreported in Africa. We present clinical features, management, and outcomes of bilateral orbital adult onset juvenile xanthogranuloma. CASE PRESENTATION A 27 year old Nigerian woman presented with bilateral upper-lid lumps...

Juvenile xanthogranuloma (JXG xanthogranulomas (JXGs) are asymptomatic; benign; self papules and nodules composed of histiocytic cells. Most common site of occurrence is skin of the head and neck region and trunk but occurrence at rare sites iris of the eye, anterior abdominal wall and tibia had been reported in literature. common form of non–Langerhans cell histiocytosis. Approximately 35% of ...

Juvenile xanthogranuloma (JXG) is a rare histiocytic disorder that typically affects children. The clinical presentation of this disease is characterized by single or, rarely, multiple yellow and brown skin nodules, most often found on the face and neck. Internal organ involvement has been sporadically observed in JXG and is associated with an increased risk of serious complications. We report ...