نتایج جستجو برای: lhermitte duclos disease
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Lhermitte-Duclos disease (dysplastic gangliocytoma of the cerebellum) is a rare benign cerebellar mass of unknown etiology which is characterized by enlargement of the cerebellar folia. Despite the controversy regarding its pathogenesis, imaging and histopathological findings are rather typical. A 17-year-old female presented with a 2-year history of progressive headaches and gait imbalance. Cr...
lhermitte - duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar lesion which share features of both malformation and neoplasm. the usual presentation is of raised intracranial pressure along with cerebellar signs. we report a case of 23 year male who presented with headache & diplopia. mri was suggestive of the diagnosis. subtotal excision of th...
Cowden syndrome and Lhermitte-Duclos disease in a family: a single genetic syndrome with pleiotropy?
Cowden syndrome is an autosomal dominant condition of multiple hamartomas. Patients with this phakomatosis have an increased risk of breast cancer and thyroid tumours. Lhermitte-Duclos disease is usually a sporadic condition of cerebellar ganglion cell hypertrophy, ataxia, mental retardation, and self-limited seizure disorder. We describe a three generation family with Cowden syndrome and Lherm...
A case of surgically confirmed Lhermitte-Duclos disease demonstrated contrast enhancement on MR. Histologic examination verified corresponding increased vascularity in the molecular layer and adjacent leptomeninges.
Since 1920, when Lhermitte and Duclos first described a tumorlike abnormality of the cerebellum, which has come to bear their name, there has been an increasing number of reports of this rare entity [1-10]. Most cases have not had radiographic correlation , but there are several reported cases in which CT was part of the pretreatment evaluation [2-7], and one case was demonstrated on low-field ...
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