نتایج جستجو برای: macrocephaly

تعداد نتایج: 695  

Journal: :Neuropsychologia 2009
Sarah White Helen O'Reilly Uta Frith

Autism is thought to be associated with a bias towards detail-focussed processing. While the cognitive basis remains controversial, one strong hypothesis is that there are high processing costs associated with changing from local into global processing. A possible neural mechanism underlying this processing style is abnormal neural connectivity; specifically reduced structural or functional con...

Journal: :American journal of medical genetics. Part B, Neuropsychiatric genetics : the official publication of the International Society of Psychiatric Genetics 2007
Joseph D Buxbaum Guiqing Cai Pauline Chaste Gudrun Nygren Juliet Goldsmith Jennifer Reichert Henrik Anckarsäter Maria Rastam Christopher J Smith Jeremy M Silverman Eric Hollander Marion Leboyer Christopher Gillberg Alain Verloes Catalina Betancur

Mutations in the PTEN gene are associated with a broad spectrum of disorders, including Cowden syndrome (CS), Bannayan-Riley-Ruvalcaba syndrome, Proteus syndrome, and Lhermitte-Duclos disease. In addition, PTEN mutations have been described in a few patients with autism spectrum disorders (ASDs) and macrocephaly. In this study, we screened the PTEN gene for mutations and deletions in 88 patient...

Journal: :Pediatric Neurology Briefs 2003

Journal: :American Journal of Medical Genetics Part A 2008

Journal: :Seminars in neurology 2015
Kellen D Winden Christopher J Yuskaitis Annapurna Poduri

Megalencephaly is a developmental disorder characterized by brain overgrowth secondary to increased size and/or numbers of neurons and glia. These disorders can be divided into metabolic and developmental categories based on their molecular etiologies. Metabolic megalencephalies are mostly caused by genetic defects in cellular metabolism, whereas developmental megalencephalies have recently bee...

2009
Jesus E Dueñas-Arias Eliakym Arámbula-Meraz Luis O Frías-Castro Rosalio Ramos-Payán Jose A Quibrera-Matienzo Fred Luque-Ortega E Maribel Aguilar-Medina

INTRODUCTION Macrocephaly-capillary malformation syndrome is characterized by cutaneous vascular lesions, including cutis marmorata telangiectatica and hemangiomas, associated with congenital anomalies, including macrocephaly, macrosomia, asymmetry and mental retardation. In addition to these cardinal signs, several other clinical conditions have been reported in people with this condition. How...

2006
Yoshihiko TAKAHASHI Yutaka TAJIMA Akira OKURA Takashi TOKUTOMI Minoru SHIGEMORI

Multi-stage reduction cranioplasty was performed on two children with severe macrocephaly sec ondary to hydrocephalus. One patient underwent a four-stage operation, and the other underwent a two-stage operation. The postoperative course of both patients was uneventful. Reduction cranioplasty improved quality of life for both patients, and good cosmetic results were achieved. Reduction craniopla...

Journal: :Neuron 2006
Joy M. Greer Anthony Wynshaw-Boris

In a comprehensive set of experiments in this issue of Neuron, Kwon et al. demonstrate that conditional inactivation of Pten leads to behavioral abnormalities and neuropathological changes. Pten mutants displayed reduced social interaction and heightened responses to sensory stimuli. Additionally, neuronal hypertrophy, as well as macrocephaly was observed. Based on rare human mutations in PTEN ...

2014
Goun Jeong Minkyun Kim Byoung Hee Han

PURPOSE This study aimed to investigate the clinical features of macrocephaly at birth in Korea using ultrasonography. METHODS We retrospectively investigated the medical records of full-term birth neonates in Cheil General Hospital & Women's Healthcare Center from January 2000 to June 2012. The following parameters were recorded and analyzed: gestational age, sex, birth weight, height, occip...

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