Rothmund–Thomson syndrome is a rare autosomal recessive genodermatosis characterized by early onset of poikiloderma and several other cutaneous and organ involvements. We are going to report a 14-year-old girl who has been diagnosed with Rothmund– Thomson syndrome since she was 3 years old and has been suffering from pain and swelling of the right elbow and forearm for about 6 months. There are...

Malignant Fibrous Histiocytoma (MFH) is the most common soft-tissue sarcoma which predominantly surfaces in the retro-peritoneum and extremity. MFH of lung is a very rare condition. The diagnosis is essentially through histologic examination. However, the invasion of the chest wall or other organs might help establish the malignant nature.We report a case of a 77-year-old man who had been prese...

Soft tissue sarcoma arising as a head and neck lesion is very rare in adults. Therefore, no standardized treatment exists for this entity of disease. We retrospectively analyzed 11 cases of head and neck soft tissue sarcomas treated at Osaka University Hospital from 1991 to 2011. They were pathologically classified as follows: 5 cases with rhabdomyosarcoma, 2 cases with liposarcoma, 2 cases wit...

introduction: myxofibrosarcoma was originally described as the myxoid variant of malignant fibrous histiocytoma (mfh), a high-grade and aggressive sarcoma, which is very uncommon in the head and neck region, with about 100 cases reported up to now. mfh occurring in the maxillary sinus is so rare that only 23 cases have been reported. we hereby report a case of myxofibrosarcoma in the maxillary ...

background & aim: malignant fibrous histiocytoma (mfh), is the most common soft tissue sarcoma in adults and is frequently seen is elderly. this lesion is so rare in bones and if seen, is common in long bones and the incidence of the lesion in maxillofacial bones is uncommon. in addition, maxilla is an unusual site for malignant fibrous histiocytoma (mfh). the aim of this article was to report ...

BACKGROUND To report six cases of CD34+ fibroblastic mesenchymal tumours, which are uncommon neoplasms in the orbit. CASE PRESENTATION Six patients presenting with proptosis and palpable mass who were later diagnosed with fibrous solitary tumours, fibrous histocytoma or haemangiopericytoma in the orbit were included. All patients received radiologic examinations and surgical excision for hist...