نتایج جستجو برای: myelofibrosis

تعداد نتایج: 4073  

Journal: :Cancer research 2015
Christophe Martinaud Christophe Desterke Johanna Konopacki Lisa Pieri Frédéric Torossian Rachel Golub Sandrine Schmutz Adrienne Anginot Bernadette Guerton Nathalie Rochet Patricia Albanese Emilie Henault Olivier Pierre-Louis Jean-Baptiste Souraud Thierry de Revel Brigitte Dupriez Jean-Christophe Ianotto Marie-Françoise Bourgeade Alessandro M Vannucchi Jean-Jacques Lataillade Marie-Caroline Le Bousse-Kerdilès

Primary myelofibrosis is a myeloproliferative neoplasm that is a precursor to myeloid leukemia. Dysmegakaryopoiesis and extramedullary hematopoiesis characterize primary myelofibrosis, which is also associated with bone marrow stromal alterations marked by fibrosis, neoangiogenesis, and osteomyelosclerosis. In particular, contributions to primary myelofibrosis from mesenchymal stromal cells (MS...

Journal: :JCI insight 2017
Lindsay Am Rein James W Wisler Jihee Kim Barbara Theriot LiYin Huang Trevor Price Haeyoon Yang Minyong Chen Wei Chen Dorothy Sipkins Yuri Fedoriw Julia Kl Walker Richard T Premont Robert J Lefkowitz

Primary myelofibrosis is a myeloproliferative neoplasm associated with significant morbidity and mortality, for which effective therapies are lacking. β-Arrestins are multifunctional adaptor proteins involved in developmental signaling pathways. One isoform, β-arrestin2 (βarr2), has been implicated in initiation and progression of chronic myeloid leukemia, another myeloproliferative neoplasm cl...

Journal: :Journal of clinical oncology : official journal of the American Society of Clinical Oncology 2011
Pamela S Becker

INCB018424, a JAK1 and JAK2 inhibitor, in myelofibrosis. N Engl J Med 363(12):1117-1127, 2010 4. Pardanani A, Gotlib JR, Jamieson C, et al: Safety and efficacy of TG101348, a selective JAK2 inhibitor, in myelofibrosis. J Clin Oncol 29:789796, 2011 5. Santos FP, Kantarjian HM, Jain N, et al: Phase 2 study of CEP-701, an orally available JAK2 inhibitor, in patients with primary or post-polycythem...

2013
Edy Hasrouni Heesun J Rogers Ali Tabarroki Valeria Visconte Fabiola Traina Manuel Afable Mikkael A Sekeres Jaroslaw P Maciejewski Ramon V Tiu

INTRODUCTION Autoimmune myelofibrosis is an uncommon hematologic disease characterized by anemia, bone marrow myelofibrosis, and an autoimmune feature. Myelofibrosis is often associated with other conditions, including infections, nutritional/endocrine dysfunction, toxin/drug exposure, and connective tissue diseases, including scleroderma and systemic lupus erythematosus. Absence of clonal mark...

Journal: :Haematologica 2016
Christina Hart Sabine Klatt Johann Barop Gunnar Müller Roland Schelker Ernst Holler Elisabeth Huber Wolfgang Herr Jochen Grassinger

Myelofibrosis is a myeloproliferative neoplasm that results in cytopenia, bone marrow fibrosis and extramedullary hematopoiesis. Allogeneic hematopoietic stem cell transplantation is the only curative treatment but is associated with a risk of delayed engraftment and graft failure. In this study, patients with myelofibrosis (n=31) and acute myeloid leukemia (n=31) were analyzed for time to engr...

Journal: :Turkish journal of haematology : official journal of Turkish Society of Haematology 2009
Zekai Avcı Barış Malbora Meltem Gülşan Feride Iffet Şahin Bülent Celasun Namık Özbek

Acute myelofibrosis is characterized by pancytopenia of sudden onset, megakaryocytic hyperplasia, extensive bone marrow fibrosis, and the absence of organomegaly. Acute myelofibrosis in patients with acute lymphoblastic leukemia is extremely rare. We report a 4-year-old boy who was diagnosed as having acute massive myelofibrosis and acute lymphoblastic leukemia. Performing bone marrow aspiratio...

2010
Kumiko Tamaki Michiro Otaka Naoto Sakamoto Kenshi Matsumoto Shunhei Yamashina Sumio Watanabe

INTRODUCTION Idiopathic myelofibrosis is a chronic myeloproliferative disorder characterized by leukoerythroblastosis, massive splenomegaly, and increases in the reticular and collagen fibers in the bone marrow. Portal hypertension is observed in some patients with idiopathic myelofibrosis. Gastrointestinal hemorrhages, which are due mostly to the rupture of the esophageal varices, have been sp...

2012
Prem Singh Ankita Goyal Deeba Mushtaq Jyoti Bala

Introduction: Tuberculosis and myelofibrosis (MF) are reported to co­exist. There seems to be a definite relationship between the two entities, possibly tuberculosis stimulating a secondary fibrotic reaction. Occurrence of myelofibrosis in Down’s syndrome has also been increasingly recognized. The purpose of this article is to present a unique case of Down’s syndrome who developed myelofibrosis...

2014
Hans Carl Hasselbalch Vibe Skov Thomas Stauffer Larsen Mads Thomassen Caroline Hasselbalch Riley Morten K. Jensen Ole Weis Bjerrum Torben A. Kruse

Identifying a distinct gene signature for myelofibrosis may yield novel information of the genes, which are responsible for progression of essential thrombocythemia and polycythemia vera towards myelofibrosis. We aimed at identifying a simple gene signature - composed of a few genes - which were selectively and highly deregulated in myelofibrosis patients. Gene expression microarray studies hav...

Journal: :Haematologica 2007
Eva Zetterberg Alessandro M Vannucchi Anna Rita Migliaccio William Vainchenker Micheline Tulliez Renée Dickie Hans Hasselbalch Rick Rogers Jan Palmblad

BACKGROUND AND OBJECTIVES Myelofibrotic bone marrow displays abnormal angiogenesis but the pathogenic mechanisms of this are poorly understood. Since pericyte abnormalities are described on solid tumor vessels we studied whether vessel morphology and pericyte coverage in bone marrow samples from patients with myelofibrosis differed from that in samples from controls. DESIGN AND METHODS We ass...

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