Fibrous dysplasia is a benign fibro-osseous lesion progressing with one or more bone involvements in the skeleton. Even though it is a benign tumor, it may potentially transform into a malignant one. While the most frequently involved zones in the head-neck zone include the maxilla, mandible, parietal, occipital, and temporal zones, the involvement of the ethmoid bone is rather rare. This artic...

Fibrous dysplasia (FD) is a relatively uncommon disorder that affects primarily the cranial region; its occurrence in the cranial base in combination with hindbrain herniation and aneurysmal bone cyst (ABC) constitutes an extremely rare condition. We report a case of polyostotic fibrous dysplasia with progressive occipital, temporal, and clival involvement. Clinical findings and differential di...

Yiş U, Dixit V, Işıkay S, Karakaya M, Baydan F, Diniz G, Polat İ, Hız-Kurul S, Çırak S. Occipital cortex dysgenesis with white matter changes due to mutations in Laminin a2. Turk J Pediatr 2017; 59: 338-341. Laminin α2 related congenital muscular dystrophy is one of the most common congenital muscular dystrophies of childhood with or without clinical evidence of central nervous system involveme...

occipital neuralgia is a condition manifested by chronic occipital headaches and is thought to be caused by irritation or trauma to the greater occipital nerve (gon). treatment for occipital neuralgia includes medications, nerve blocks, and pulsed radiofrequency ablation (prfa). landmark-guided gon blocks are the mainstay in both the diagnosis and treatment of occipital neuralgia. ultrasound is...

Case presentation: Female, 8 years old, with onset of seizures at 2 months, evolving refractory epilepsy. The were characterized by behavioral arrest and vacant gaze, in addition to episodes loss tone head turn the right intense salivation. Patient has used topiramate, nitrazepam, carbamazepine valproate. On examination, he is moderately mentally retarded does not speak. Prolonged videoelectroe...

syndrome. The cerebellum within those cephaloceles is usually dysplastic and gliotic. Plexiform NF, hallmark of NF-I are found in 30-40% of all patients with NF-I. They usually arise along the axis of a major nerve, are unencapsulated and infiltrate producing fusiform appearance. They commonly occur along orbital division of V nerve, but other areas are not exempt often associated with sphenoid...