Primary intestinal lymphangiectasia or Waldmann's disease is an uncommon cause of protein losing enteropathy with an unknown etiology and is usually diagnosed during childhood. It is characterized by dilation and leakage of intestinal lymph vessels leading to hypoalbuminemia, hypogammaglobulinemia and lymphopenia. Differential diagnosis should include erosive and non-erosive gastrointestinal di...

Primary intestinal lymphangiectasia (PIL) is a rare protein-losing gastroenteropathy characterized by dilatation of the lymphatics and loss lymph fluid into gastrointestinal tract, leading to development hypoproteinaemia, oedema, lymphocytopenia, hypogammaglobinaemia, immunologic abnormalities. We report series 4 children from Bangalore, India presenting with anasarca, diarrhoea, hypoproteinaem...

ture was referred by the orthopedic department at our hospital for severe hypoproteinemia. The patient had been diagnosed as having primary intestinal lymphangiectasia at the age of 25. Under capsule endoscopy, numerous filiformlike polyps with whitish villi were observed from the distal duodenum to the jejunum (●" Fig. 1a) with exudation of a chylous substance from the mucosal surface (●" Fig....

Primary intestinal lymphangiectasia (PIL), Waldmann's disease, is a rare disorder of unknown etiology characterized by dilated intestinal lacteals leading to lymph leakage into the small-bowel lumen and responsible for protein-losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia. PIL is generally diagnosed before 3 years of age but may be diagnosed in older patie...

UNLABELLED Primary intestinal lymphangiectasia is an uncommon congenital anomaly. It is an intrinsic abnormality of the intestinal lymphatics system. Over the years, various treatment options such as diuretics, albumin transfusions and a medium chain triglycerides (MCT) diet as well as surgical options such as resection of isolated segments and peritoneal-venous shunts have been used. An MCT di...

Primary intestinal lymphangiectasia is a rare disease of the intestinal lymphatics, presenting with protein-losing enteropathy, hypoproteinemia, bilateral lower limb edema, and ascites [1–4]. Here we report capsule endoscopic findings in a patient with primary intestinal lymphangiectasia. A 51-year-old woman was admitted due to swelling of her legs and abdomen, and shortness of breath for nearl...

Intestinal lymphangiectasia is a disease characterized by dilated intestinal lymphatics, protein-losing enteropathy, hypoalbuminemia, and edema. The immunologic status of 18 patients with intestinal lymphangiectasia was studied. Concentrations of IgG, IgA, and IgM were measured by immune precipitation and metabolism of these three immunoglobulins was studied using purified radioiodinated protei...