We report the accurate prenatal diagnosis at 22 weeks gestation of right atrial isomerism in association with tricuspid atresia. Several distinctive sonographic features of isomerism of the right atrial appendages were present in this fetus: complex cardiac abnormality, ventriculoarterial discordance, juxtaposition of the aorta and the inferior vena cava to the right side, pulmonary atresia, an...

a four month old male infant was referred to the pediatric clinic of afshar hospital in yazd city because of cyanosis. on physical examination, patient had central cyanosis, single second heart sound, a grade iii/vi continuous murmur in left clavicular area, abdominal distension and large sized smooth and movable abdominal mass in right upper quadrant of abdomen. transthoracic echocardiography ...

BACKGROUND In our practice, we noticed an increased frequency of tracheobronchial branching abnormalities (TBAs) in patients with tetralogy of Fallot (ToF). This study aimed to determine whether an association exists between congenital TBAs and ToF with or without pulmonary atresia. METHODS AND RESULTS The frequency of TBAs on chest computed tomography was assessed in 55 patients with ToF wit...

the aim of this study is to evaluate early and late results of surgery in children with congenital heart disease and decreased pulmonary blood flow, who underwent a palliative systemic-to-pulmonary shunt. during the past 9 years, 157 systemic-to-pulmonary artery shunts were performed in 130 patients (69 males, 61 females) with ages from 1 day to 31 years old. they had been evaluated for their c...

OBJECTIVE To identify the types of pulmonary vascular blood supply in tetralogy of Fallot with pulmonary atresia by use of hemodynamic study. METHODS Fifty-six patients with tetralogy of Fallot and pulmonary atresia, and ages ranging from 20 days to 4 years, underwent cineangiocardiographic study with contrast medium injections in the following vascular structures: 1) wedged pulmonary vein; 2...

Bilateral ductal stenting should be performed in cases of discontinuity of the pulmonary branches and pulmonary atresia. Performing this procedure via the carotid artery in small infants can be very difficult and challenging. We present a case of bilateral ductal stenting via both the femoral and carotid arteries in a little child with tetralogy of Fallot with pulmonary atresia and a nonconflue...

Submit Manuscript | http://medcraveonline.com clinical manifestations depends on the amount of collateral blood flow and the presence of an associated congenital heart defect [3]. Unilateral PVA has been reported in children and adult patients [3,4]. A particular condition of unilateral pulmonary vein atresia with atresia of the contralateral upper pulmonary vein in a child who died at the age ...

The aim of this study was to evaluate whether MR could depict pulmonary arterial anatomy in more detail than routine angiography in patients with congenital interruption or acquired occlusion of the left pulmonary artery or pulmonary atresia. This study included 10 patients with tetralogy of Fallot (n=6) or pulmonary atresia with ventricular septal defect (n=3) or aorticopulmonary window (n=1) ...

Xenon-133 lung ventilation and perfusion scans were done preoperatively after cardiac catheterization and cineangiocardiography in 19 children; 6 had pulmonary atresia with an intact ventricular septum and hypoplastic right ventricle, 4 pulmonary atresia with associated complex univentricular heart, and 9 extreme Tetralogy of Fallot. The four patients with discrepancies in the sizes of the left...

Forty cases of left atrioventricular valve (LAV) atresia without aortic stenosis or atresia were reviewed. Thirty-one had mitral atresia and nine had left tricuspid atresia. Eleven had associated pulmonary outflow tract obstruction. Twenty-two (55%) underwent cardiac catheterization and 12 had more than one study. Left atrial pressure was normal in seven infants younger than 2 weeks of age. Twe...