نتایج جستجو برای: rare bleeding disorder

تعداد نتایج: 857287  

Journal: :Pediatric Hematology Oncology Journal 2018

Journal: :Journal of Evolution of Medical and Dental Sciences 2020

Akbar Dorgalaleh, Farhad Zaker, Hasan Mollanoori, Hojat Shahraki, Majid Fathi, Maryam Daneshi, Omolbanin Sargazi-Aval, Shadi Tabibian, Shahram Teimourian,

Background: Congenital factor XIII (FXIII) deficiency is one of the rarest bleeding disorders with a prevalence of one per 2 million in the general population. The disorder is accompanied by a high rate of life-threatening bleeding. Due to normal results of routine coagulation tests, diagnosis of the disorder is challenging, but molecular methods can be used for precise diagnosis. Direct mutati...

Journal: :journal of comprehensive pediatrics 0
mojtaba vahid golpayegani department of pediatric dentistry, school of dentistry, shahid beheshti university of medical sciences, tehran, ir iran hossein behnia department of oral & maxillofacial surgery, school of dentistry, shahid beheshti university of medical sciences, tehran, ir iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences) mahvareh akhgar araghi pedodontist, tehran, ir iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences) ghassem ansari department of pediatric dentistry, school of dentistry, shahid beheshti university of medical sciences, tehran, ir iran; department of pediatric dentistry, school of dentistry, shahid beheshti university of medical sciences, tehran, ir iran. tel: +98-21 22255537

conclusions the case was fully investigated and diagnosed as a case with factor xiii deficiency causing such uncontrolled bleeding after extraction of a tooth. introduction factor xiii deficiency is a relatively rare hereditary bleeding disorder, which is usually found during infancy or early childhood. this condition may involve both genders within different races in an equal manner. its incid...

Journal: :International journal of advanced research 2022

Glanzmann thrombasthenia is a rare genetic disorder. It of autosomal inheritance. usually presents as ecchymoses, petechiae, gum bleeding, musical and menorrhagia. An acute episode bleeding can be managed with intravenous antifibrinolytics, blood products transfusion later hormonal therapy. Newer modalities include Recombinant factor VIIa. A multidisciplinary approach needed for the diagnosis m...

2008
Matthew T. Hurford Christopher Sebastiano

Hermansky-Pudlak syndrome is a rare autosomal recessive disorder characterized by excessive bleeding post surgery. Here we reported such a case and reviewed the clinicopathological features and our current understanding of this rare congenital disorder.

Journal: :International journal of clinical and experimental pathology 2008
Matthew T Hurford Christopher Sebastiano

Hermansky-Pudlak syndrome is a rare autosomal recessive disorder characterized by excessive bleeding post surgery. Here we reported such a case and reviewed the clinicopathological features and our current understanding of this rare congenital disorder.

Journal: :international journal of hematology-oncology and stem cell research 0
ali naderi pediatric hematology- oncology department, kerman university of medical sciences, kerman, iran mohmmadreza ebadzadeh urology department, kerman university of medical sciences, kerman, iran jalal azmandyan nephrology, kerman university of medical sciences, kerman, iran razieh fayazfar hemophilia center of afzalipour hospital, kerman university of medical sciences, kerman, iran elham ahmadi pediatric ward, kerman university of medical sciences, kerman, iran ali rikhtehgaran tehrani researcher, kerman university of medical sciences, kerman, iran

introduction: the prevalence of rare bleeding disorders, including combined factor v+viii deficiency are higher in iran than in developed countries. there are only a few reports which have been written concerning kidney transplantation in the patients suffering from these disorders. case report: a 22-year old girl, with a known case of combined factor v+viii deficiency, a history of bladder sto...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید