congenital hepatic fibrosis (chf) is a developmental disorder of the biliary system, characterized by defective remodeling of the ductal plate. herein a family of three children, from consanguineous parents, with minor thalassemia is presented who suffered from congenital hepatic fibrosis (chf). prompt diagnosis and appropriate treatment are necessary to avoid further complications in the affec...

Gastrointestinal (GI) bleeding is a common complication of cirrhosis and portal hypertension. Most cases are secondary to gastro-esophageal variceal rupture, managed endoscopically1. Stomal rare there’s no standard therapy2. We present case cirrhotic patient with recurrent stomal hemorrhage successfully treated transjugular intrahepatic portosystemic shunt (TIPS) varices embolization.

2. Visani G, Finelli C, Castelli U, et al. Myelofibrosis with myeloid metaplasia: clinical and haematological parameters predicting survival in a series of 133 patients. Br J Haematol. 1990;75:4-9. 3. Shaldon S, Sherlock S. Portal hypertension in the myeloproliferative syndrome and the reticuloses. Am J Med. 1962;32:758-764. 4. Rossle M, Siegerstetter V, Huber M, Ochs A. The first decade of the...

459 Most of the morbidity associated with chronic liver disease results from the development of portal hypertension and its sequelae. Transjugular intrahepatic portosystemic shunt (TIPS) is a minimally invasive method of creating a portosystemic shunt that can effectively decompress the hypertensive portal circulation and treat its complications. Introduced more than a decade ago, the procedure...

Surgery for portal hypertension began in 1877, with Nicolai Vladirmirovich who performed the fi rst portacaval anastomosis. There was little clinical success until Blakemore and Whipple between the 1920’s and 1940’s: the mortality rate ranged from 25-40%. Hepatic encephalopathy was a clinical problem. In 1960, Warren and collegues performed a distal splenorenal shunt, which reduced the incidenc...

a 43-year-old man with liver cirrhosis received transjugular intrahepatic portosystemic shunt (tips) for the treatment of recurrent variceal bleeding and f3 esophageal varices. during routine follow up liver ultrasound examination, six months after the implantation, tips occlusion was suspected and tips revision was performed. during the revision, moderate to severe stenosis at the hepatic veno...

BACKGROUND/AIMS The purpose of this study was to evaluate the technical/hemodynamic success, complications, and biochemical/ hematologic consequences of transjugular intrahepatic portosystemic shunt (TIPS) created with 10-mm bare stents in our patients. MATERIALS AND METHODS Data of 27 cirrhotic patients (18 men and 9 women; mean age, 39.7±18.7 years) with a median MELD score 14 (range 7-31) ...

1. Episodic (precipitant-induced) encephalopathy, commonly seen in the hospital setting, where a superimposed event is a key factor. 2. Persistent (chronic) encephalopathy, seen with extensive portal–systemic shunts and after portocaval shunt surgery or placement of transjugular intrahepatic portosystemic shunt (TIPS). 3. Minimal (subclinical) encephalopathy reflects alterations in cognitive fu...

HYPOTHESIS Distal splenorenal shunt (DSRS) is a safe and effective treatment for patients with Child-Pugh class A and B cirrhosis with recurrent variceal hemorrhage after failed transjugular intrahepatic portosystemic shunt. DESIGN Retrospective case review. SETTING Hepatobiliary surgery and liver transplantation department in a tertiary referral medical center. PATIENTS Between August 1,...