Vulvar lymphangioma circumscriptum (LC) is a rare entity which may present as a painful, warty lesion. In contrast to the congenital form, which occurs in children, the acquired form arises in older adults and may be associated with infection, Crohn's disease, or prior pelvic/regional surgery. We present a case of acquired LC of the vulva in a 55-year-old woman who presented with a 3-4 year his...

Lymphangioma circumscriptum is a rare disorder of lymphatic channels characterised by multiple grouped thin translucent vesicles. The lesions are often seen around the neck, upper trunk, proximal extremities and tongue. Genital involvement in females has been reported but penis is a rare site. On the other side congenital variety is extremely rare. Here we are presenting a rare case of congenit...

Lymphangioma circumscriptum of the vulva is a disorder of lymphatic channels involving deep dermal tissues. Most of these cases are confused with genital warts leading to improper diagnosis and treatment. We present a three years young female child who had multiple skin colored papular lesions over the genitals. Skin biopsy revealed features of lymphangioma circumscriptum.

To the Editor: Lymphangioma circumscriptum (LC) is not a tumor but rather a congenital malformation of the superficial lymphatics. It presents as groups of deep-seated, vesicle-like papules, resembling frog spawn, at birth or shortly thereafter. Also, the sites of predilection are the abdomen, axillae, genitalia, and mouth, particularly the tongue.[1] Klippel-Trenaunay syndrome (KTS) is relativ...

Lymphangioma circumscriptum (LC) is an abnormal saccular dilatation of lymph ducts in the skin, subcutaneous tissue and deep dermal layer. Proximal extremities, trunk, axilla, buttocks and oral cavity are some common sites of involvement. Vulval involvement is extremely uncommon. It can be developmental or acquired [1]. We describe a very rare case of lymphangioma circumscriptum involving the v...

Lymphangiomas are congenital lymphatic malformations and cutaneous lymphangioma circumscriptum is the most common type. It is clinically characterized by clusters of translucent vesicles and the presence of dermoscopically yellow lacunae surrounded by pale septa, as well as reddish to bluish lacunae. In our case, the recently described hypopyon-like feature manifested, aiding in the sometimes d...

HS: hidradenitis suppurativa LC: lymphangioma circumscriptum PP: pseudoverrucous papules SCC: squamous cell carcinoma INTRODUCTION Acquired lymphangioma circumscriptum (LC), also known as localized LC, is characterized by small, clear, fluid-filled, clustered vesicles and papules that resemble a gelatinous mass of ‘‘frog spawn’’ on the surface of the skin. We present a case of genital LC associ...

Lymphangioma circumscriptum is a benign disease of the lymph ducts and an unusual pathologic process that rarely affects the vulva. The etiology of this lesion is not clear, but obstruction of the lymph vessels has been suggested as a possible cause in some cases. We report the case of a 44-year-old woman with lesions similar to lymphangioma circumscriptum of the vulva and chronic idiopathic ly...

OBJECTIVE To promote proper identification and management of this rare entity by presenting a review of the literature, a case report, and illustrations of its presentation and pathology. DATA SOURCES Sources searched included the literature contained in the National Library of Medicine's PubMed database, using the term "lymphangioma circumscriptum" combined with "vulva." Other search terms u...