نتایج جستجو برای: carnitine palmitoyltransferase 1a

تعداد نتایج: 38168  

Journal: :American journal of physiology. Heart and circulatory physiology 2003
Arzu Onay-Besikci Fiona M Campbell Teresa A Hopkins Jason R B Dyck Gary D Lopaschuk

After birth, a dramatic increase in fatty acid oxidation occurs in the heart, which has been attributed to an increase in l-carnitine levels and a switch from the liver (L) to muscle (M) isoform of carnitine palmitoyltransferase (CPT)-1. However, because M-CPT-1 is more sensitive to inhibition by malonyl CoA, a potent endogenous regulator of fatty acid oxidation, a switch to the M-CPT-1 isoform...

2017
Sabrina Mucerino Anna Di Salle Nicola Alessio Sabrina Margarucci Raffaella Nicolai Mariarosa A. B. Melone Umberto Galderisi Gianfranco Peluso

Rett syndrome (RTT) is a neurodevelopmental disease that leads to intellectual deficit, motor disability, epilepsy and increased risk of sudden death. Although in up to 95% of cases this disease is caused by de novo loss-of-function mutations in the X-linked methyl-CpG binding protein 2 gene, it is a multisystem disease associated also with mitochondrial metabolic imbalance. In addition, the pr...

1998
THERESA M. VISARIUS HEINZ BÄHLER ADRIAN KÜPFER THOMAS CERNY BERNHARD H. LAUTERBURG

Thiodiglycolic acid has been identified as a major metabolite of the anticancer drug ifosfamide in humans. Patients treated with 12–16 g ifosfamide/mzday excreted thiodiglycolic acid ranging from 0.10 6 0.02 mmol on the first day of therapy, to a maximum of 3.27 6 0.15 mmol on the fourth day of ifosfamide infusion. This amounted to 5.4 6 0.2% of the administered dose of ifosfamide appearing as ...

2014
Paula Mera Joan Francesc Mir Gemma Fabriàs Josefina Casas Ana S. H. Costa Maria Ida Malandrino José-Antonio Fernández-López Xavier Remesar Su Gao Shigeru Chohnan Maria Sol Rodríguez-Peña Harald Petry Guillermina Asins Fausto G. Hegardt Laura Herrero Dolors Serra

Lipid metabolism in the ventromedial hypothalamus (VMH) has emerged as a crucial pathway in the regulation of feeding and energy homeostasis. Carnitine palmitoyltransferase (CPT) 1A is the rate-limiting enzyme in mitochondrial fatty acid β-oxidation and it has been proposed as a crucial mediator of fasting and ghrelin orexigenic signalling. However, the relationship between changes in CPT1A act...

Journal: :The Journal of experimental biology 1991
A Tullis B A Block B D Sidell

Maximal in vitro activities of key metabolic enzymes were measured in brain and eye heaters of five species of scombroid fishes. Istiophorid billfishes (blue marlin, striped marlin and Mediterranean spearfish), xiphiid billfishes (Pacific and Mediterranean stocks) and a scombrid fish (butterfly mackerel) were included in the analysis. Our main objectives were (1) to assess the maximum possible ...

Journal: :American journal of physiology. Regulatory, integrative and comparative physiology 2015
Cecilia Ratner Andreas Nygaard Madsen Line Vildbrad Kristensen Louise Julie Skov Katrine Seide Pedersen Ole Hartvig Mortensen Gitte Moos Knudsen Kirsten Raun Birgitte Holst

To characterize mechanisms responsible for fat accumulation we used a selectively bred obesity-prone (OP) and obesity-resistant (OR) rat model where the rats were fed a Western diet for 76 days. Body composition was assessed by magnetic resonance imaging scans, and as expected, the OP rats developed a higher degree of fat accumulation compared with OR rats. Indirect calorimetry showed that the ...

Journal: :The Biochemical journal 1995
M Guzmán C Bijleveld M J Geelen

Periportal and perivenous hepatocytes were isolated from rats subjected to different treatments that induce (starvation, cold exposure) or depress (refeeding after starvation) hepatic fatty acid oxidation. These experiments were designed to determine factors that may be involved in creating and maintaining the asymmetrical distribution of this metabolic pathway in the acinus of the liver. The u...

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