نتایج جستجو برای: clinical exome sequencing

تعداد نتایج: 1271061  

Journal: :Circulation 2013
Bryce A Schuler Sasha Z Prisco Howard J Jacob

W hole exome sequencing (WES) is currently used to identify the genetic causes of many diseases, especially monogenic disorders. Ng et al, 1 in 2009, completed the first proof-of-principle study demonstrating the feasibility of using exome sequencing to identify causal variants for diseases, specifically Freeman-Sheldon syndrome. Within 2 years, there was a marked increase in publications prese...

2015
Maxime G Blanchard Marjolein H Willemsen Jaclyn B Walker Sulayman D Dib-Hajj Stephen G Waxman Marjolijn CJ Jongmans Tjitske Kleefstra Bart P van de Warrenburg Peter Praamstra Joost Nicolai Helger G Yntema René JM Bindels Miriam H Meisler Erik-Jan Kamsteeg

BACKGROUND Mutations of SCN8A encoding the neuronal voltage-gated sodium channel NaV1.6 are associated with early-infantile epileptic encephalopathy type 13 (EIEE13) and intellectual disability. Using clinical exome sequencing, we have detected three novel de novo SCN8A mutations in patients with intellectual disabilities, and variable clinical features including seizures in two patients. To de...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2015
Aziz Belkadi Alexandre Bolze Yuval Itan Aurélie Cobat Quentin B Vincent Alexander Antipenko Lei Shang Bertrand Boisson Jean-Laurent Casanova Laurent Abel

We compared whole-exome sequencing (WES) and whole-genome sequencing (WGS) in six unrelated individuals. In the regions targeted by WES capture (81.5% of the consensus coding genome), the mean numbers of single-nucleotide variants (SNVs) and small insertions/deletions (indels) detected per sample were 84,192 and 13,325, respectively, for WES, and 84,968 and 12,702, respectively, for WGS. For bo...

2016
Elizabeth A. Sellars Bonnie R. Sullivan G. Bradley Schaefer

Rubinstein-Taybi syndrome is associated with intellectual and physical features. CREBBP and EP300 are causative. Few cases of EP300 mutations are reported. We report a case with mild features of RSTS and EP300 mutation on exome sequencing. This illustrates the utility of exome sequencing to expand every genetic phenotype.

Journal: :Clinical cancer research : an official journal of the American Association for Cancer Research 2016
Charlotte Pawlyn Martin F Kaiser Christoph Heuck Lorenzo Melchor Christopher P Wardell Alex Murison Shweta S Chavan David C Johnson Dil B Begum Nasrin M Dahir Paula Z Proszek David A Cairns Eileen M Boyle John R Jones Gordon Cook Mark T Drayson Roger G Owen Walter M Gregory Graham H Jackson Bart Barlogie Faith E Davies Brian A Walker Gareth J Morgan

PURPOSE Epigenetic dysregulation is known to be an important contributor to myeloma pathogenesis but, unlike other B-cell malignancies, the full spectrum of somatic mutations in epigenetic modifiers has not been reported previously. We sought to address this using the results from whole-exome sequencing in the context of a large prospective clinical trial of newly diagnosed patients and targete...

Journal: :The Journal of law, medicine & ethics : a journal of the American Society of Law, Medicine & Ethics 2014
Gail E Henderson Susan M Wolf Kristine J Kuczynski Steven Joffe Richard R Sharp D Williams Parsons Bartha M Knoppers Joon-Ho Yu Paul S Appelbaum

As exome and genome sequencing move into clinical application, questions surround how to elicit consent and handle potential return of individual genomic results. This study analyzes nine consent forms used in NIH-funded sequencing studies. Content analysis reveals considerable heterogeneity, including in defining results that may be returned, identifying potential benefits and risks of return,...

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