Results In our service, a hundred and thirty patients with the diagnosis of a primary immunodeficiency are followedup and from this sample we have four patients with AT. Acessing clinical history and the laboratory findings becomes clear that a large variability occurs concerning their immune system. All subjects presented recurrent infections, especially sinopulmonary . In laboratory evaluatio...

BACKGROUND Corticobasal syndrome (CBS) is a multifaceted neurodegenerative disorder characterized by a combination of motor and cognitive deficits. Several different pathological entities, including Alzheimer's pathology, have been described in association with CBS. The present study aimed to establish clinical, neuropsychological, and neuroimaging features that could be useful in the distincti...

associated symptoms in patients with nephritis (5). Variability in these findings can be explained by the different ethnic background of the studied sample. We have studied associated symptoms in 71 patients with lupus nephritis and 142 SLE patients without renal involvement. This sample includes all lupus patients with nephritis followed in the last five years in our service, with biopsy prove...

BACKGROUND Reports on pediatric electroencephalogram of Nepalese patients are rare. OBJECTIVE We aimed to study the relationship between provisional clinical and electrophysiological diagnoses of pediatric patients with documentation of demographic profiles, and type and frequency of the disorders/diseases. METHODS Electroencephalographic reports of 634 children from 2006 to 2009 were analy...

therapy in resistant enteric fever, various drugs singly, or in combination, such as cotrimoxazole and cephalosporins, or cephalexin and gentamicin, third generation cephalosporins and newer quinolones have been tried with varying results. This communication describes our observations on the clinical profile of children with enteric fever due to MDRST infection and, compare different drug regim...

OBJECTIVES To study clinical presentation, hospital care and outcome of patients of Guillain Barre Syndrome (GBS) and number of patients of respiratory failure and need for ventilators. To study efficacy of IVIg in patients of GBS. MATERIAL AND METHODS 40 patients of GBS studied in detail including history, clinical examination and investigations (Nerve conduction velocity and C.S.F. examinat...

CONTEXT Although blunt, nonpenetrating chest blows causing sudden cardiac death (commotio cordis) are often associated with competitive sports, dangers implicit in such blows can extend into many other life activities. OBJECTIVE To describe the comprehensive spectrum of commotio cordis events. DESIGN AND SETTING Analysis of confirmed cases from the general community assembled in the US Comm...

OBJECTIVE To assess the prevalence of hypertensive crisis, related clinical findings, and the organic lesions involved. METHOD This retrospective study comprised the analysis of the medical records of symptomatic patients with an elevation in diastolic blood pressure levels > or = 120 mmHg, who sought the emergency unit of a university-affiliated hospital over 12 months. Hypertensive urgency ...

PURPOSE To report the clinical features and outcome of a series of children with optic neuritis. METHODS We reviewed the medical records of patients up to 16 years old with optic neuritis. Group 1 comprised children seen up to two weeks after the onset of visual loss; Group 2 comprised patients already harboring optic atrophy. RESULTS There were 15 boys and 12 girls. The mean age was 10.9 y...

In patients with diabetes, treatment intensification requires basal and bolus insulin injections to control the fasting and prandial insulin needs. To overcome the burden of multiple daily injections, co-formulating basal and bolus insulins in single injection could allow a simple regimen with fewer injections. Current premixed insulin analogues are limited by the protaminated insulin component...