Dear Editor, Supravalvular aortic stenosis (SVAS) is a congenital narrowing of the ascending aorta above the level of sinus of Valsalva. It is most often commonly associated with William’s syndrome although it can arise without syndromic associations as well.1,2 Left main coronary artery (LMCA) occlusion or stenosis has been seen to be associated with the condition, and can be a cause of sudden...

Isolated left ventricular (LV) apical hypoplasia is a rare congenital cardiac anomaly which is not accompanied by other cardiac abnormalities, with the exception of two cases. We report a case of a 33-year-old male patient with isolated LV apical hypoplasia combined with infundibular pulmonary stenosis and aortic stenosis. We review a literature focusing on the characteristic magnetic resonance...

we report a rare case of acute right coronary artery stenosis developing in a patient undergoing aortic valve replacement. we present a case report with a brief overview of the literature relating to coronary artery occlusion associated with cardiac valve surgery – the theories and treatments are discussed. a 85 year-old female was admitted under the care of the  cardiothoracic team with signs ...

A bicuspid aortic valve (BAV) demonstrating moderate valvular stenosis and mild insufficiency was identified in an asymptomatic 1-year-old male cryptorchid English bulldog by transthoracic and transesophageal echocardiography. The BAV was most consistent with type 3 morphology, based upon human classification. Pulmonary valve dysplasia with mild pulmonary stenosis and a suspected persistent lef...

We have reviewed the cases operated upon for correction of congenital aortic stenosis at l'Hôpital Ste-Justine between 1959 and 1969.Twenty-five of the 26 patients were readmitted for complete clinical, radiological and hemodynamic investigation. Fourteen had a valvular stenosis, eight a diaphragmatic subvalvular lesion, and three had mixed lesions.The results lead us to believe that the surgic...

OBJECTIVE To evaluate immediate and midterm results with percutaneous aortic valvoplasty. MATERIAL AND METHODS We reviewed the records of 141 patients undergoing percutaneous aortic valvopasty over a period of 13 years. RESULTS The patients were aged from 2 months to 40 years, with a mean of 10.9 +/- 9.9 years. Of the total, 90 (63+/%) were male. The initial systolic peak-to-peak gradient d...

Williams-Beuren syndrome is a rare familial multisystem disorder occurring in 1 per 20,000 live births. It is characterized by congenital heart defects (CHD), skeletal and renal anomalies, cognitive disorder, social personality disorder and dysmorphic facies. We present a case of Williams syndrome that presented to us with heart murmur and cognitive problem. A 5-year-old girl referred to pediat...

PATIENTS with bicuspid aortic valve (BAV) malformations, the most common congenital cardiac abnormality, are at significantly higher lifetime risk of developing aortic stenosis, aortic regurgitation, aortic root dilatation, infective endocarditis, aortic aneurysm, and aortic dissection. Unfortunately, once these complications develop, cardiac surgical intervention is required in the vast majori...

Piercing invades subcutaneous areas and has a high potential for infectious complications. The number of case reports of endocarditis associated with piercing is increasing. We studied a 25-year-old man with a pierced tongue, who arrived at Memorial Health University Medical Center with fever, chills, rigors, and shortness of breath of 6 days' duration and had an aortic valvuloplasty for correc...