Bilateral renal agenesis/hypoplasia/dysplasia is a lethal malformation in humans with an incidence of 1.3 per 10,000 live births. In the etiology bilateral agenesis/hypoplasia/dysplasia, genetic factor plays important role. addition to factors, also involves teratogenic effect hyperglycemia on embryo mothers insulin-dependent maternal diabetes. The purpose this paper present special case which ...

This study investigated the prevalence of enamel hypoplasia and dental caries and the relationship between the two diseases in all 4- to 6-year-old Australian Aboriginal children of the Tiwi tribe on Bathurst Island. Seventy-nine of 80 children (99%) had enamel hypoplasia, with a mean of 12.0 +/- 4.1 hypoplastic teeth per child. Dental caries was noted in 66 (83%) of children and the mean numbe...

Introduction Hypoplasia is defined as a quantitative defect of enamel visually and is histomorphologically identified as an external defect involving the surface of the enamel and associated with reduced thickness of enamel (Ozturk et al, 2004).Turner's hypoplasia usually manifests as a portion of missing or diminished enamel, generally affecting one or more permanent teeth in the oral cavity. ...

Maxillary sinus hypoplasia (MSH) is an uncommon abnormality of paranasal sinuses noted in clinical practice. Computed tomography (CT) scan helps in diagnosing the anomaly along with any anatomical variation that may be associated with it. MSH is usually associated with other anomalies like uncinate process hypoplasia. Three types of MSH have been described. Type 1 MSH shows mild maxillary sinus...

Purpose Previous reports have demonstrated diminished size of the hindfoot bones in patients with idiopathic clubfoot deformity. However, no study has quantified the percentage of hypoplasia as a function of early growth, during the brace phase of Ponseti treatment. Methods We measured the dimensions of ossified structures on radiographs in patients with unilateral Ponseti-treated clubfeet to...

DESIGN Advances in neuroimaging have allowed correlations between radiological patterns and clinical features of brain malformations. This paper reports clinical, prognosis, and electroencephalographic features of six children with a previously unrecognised neuroimaging picture of unilateral widening and verticalisation of the sylvian fossa associated with an abnormal ipsilateral perisylvian co...

Cartilage hair hypoplasia (CHH), is a rare cause of metaphyseal chondrodysplasia and short stature. Other featuresincluded hair abnormality, immunodeficiency, anemia, gastrointestinal disorders (Hirschsprung disease,celiac, …) and increased risk of cancer. The disease is an autosomal recessive disorder and previously has notbeen reported in Iran. We report a 9-year-old boy diagnosed as cartilag...

Abstract Medulloblastoma is the most common malignant brain tumor in children, accounting for 20-25% of all pediatric tumors. The current standard care includes both craniospinal and focal radiation therapy which leads to long term consequences population such as bone tissue hypoplasia, decreased neurocognitive functioning, well an increased risk secondary induced cancers. Thus, there a need no...

o bjectives: the aim of this study was to determine the cementum thickness in the first molars of patients with localized aggressive periodontitis (lap) compared to healthy individuals. materials and methods: this case-control study compared eight first molar teeth af-fected by lap with eight third molar teeth of healthy individuals. the teeth were dis- infected by immersion in 10% buffered for...