نتایج جستجو برای: hematologic neoplasms

تعداد نتایج: 507542  

Journal: :Blood 2010
Franz X Schaub Renate Looser Sai Li Hui Hao-Shen Thomas Lehmann Andre Tichelli Radek C Skoda

Somatic mutations in TET2 occur in patients with myeloproliferative neoplasms and other hematologic malignancies. It has been suggested that TET2 is a tumor suppressor gene and mutations in TET2 precede the acquisition of JAK2-V617F. To examine the order of events, we performed colony assays and genotyped TET2 and JAK2 in individual colonies. In 4 of 8 myeloproliferative neoplasm patients, we f...

Journal: :Clinical cancer research : an official journal of the American Association for Cancer Research 2012
John Mascarenhas Ronald Hoffman

The BCR-ABL1-negative myeloproliferative neoplasms (e.g., essential thrombocythemia, polycythemia vera, and primary myelofibrosis) are a group of heterogeneous hematologic malignancies that involve a clonal proliferation of hematopoietic stem cells. Thrombosis, bleeding, and transformation to acute leukemia reduce the overall survival of patients with myelofibrosis, a disease typified by progre...

Journal: :Haematologica 2013
Lucile Couronné Laurianne Scourzic Camilla Pilati Véronique Della Valle Yannis Duffourd Eric Solary William Vainchenker Jean-Philippe Merlio Marie Beylot-Barry Frederik Damm Marc-Henri Stern Philippe Gaulard Laurence Lamant Eric Delabesse Hélène Merle-Beral Florence Nguyen-Khac Michaëla Fontenay Hervé Tilly Christian Bastard Jessica Zucman-Rossi Olivier A Bernard Thomas Mercher

STAT3 protein phosphorylation is a frequent event in various hematologic malignancies and solid tumors. Acquired STAT3 mutations have been recently identified in 40% of patients with T-cell large granular lymphocytic leukemia, a rare T-cell disorder. In this study, we investigated the mutational status of STAT3 in a large series of patients with lymphoid and myeloid diseases. STAT3 mutations we...

Journal: :Journal of the American Society of Nephrology : JASN 2016
Michael B Stokes Anthony M Valeri Leal Herlitz Abdullah M Khan David S Siegel Glen S Markowitz Vivette D D'Agati

Light chain proximal tubulopathy (LCPT) is characterized by cytoplasmic inclusions of monoclonal LC within proximal tubular cells. The significance of crystalline versus noncrystalline LCPT and the effect of modern therapies are unknown. We reported the clinical-pathologic features of 40 crystalline and six noncrystalline LCPT patients diagnosed between 2000 and 2014. All crystalline LCPTs were...

Journal: :Medicina clinica 2011
Atul Mehta

Gaucher's disease (GD) is the most common lysosomal storage disease with a frequency of approximately 1:50,000 people. It is the result of the deficiency of the lysosomal enzyme beta-glucocerebrosidase. The deficiency of the enzyme results in the accumulation of the substrate, glucosyl-ceramide, in the organs. Substitutive enzymatic treatment has been available since almost 20 years. This brief...

Journal: :Blood 2010
Bruno Royer Ketty Lee Berengere Gruson France Roszkiewicz Abdullatif Al Khedr Agnes Colson Agnes Camboulives Philippe Bierling Jean Pierre Marolleau

3. Matsuda K, Shimada A, Yoshida N, et al. Spontaneous improvement of hematologic abnormalities in patients having juvenile myelomonocytic leukemia with specific RAS mutations. Blood. 2007;109(12):5477-5480. 4. Grand FH, Hidalgo-Curtis CE, Ernst T, et al. Frequent CBL mutations associated with 11q acquired uniparental disomy in myeloproliferative neoplasms. Blood. 2009;113(24):6182-6192. 5. Mat...

Journal: :Haematologica 2007
Pasquale Niscola Claudio Romani Luca Cupelli Laura Scaramucci Andrea Tendas Teresa Dentamaro Sergio Amadori Paolo de Fabritiis

Mucosal barrier injury (mucositis) is a common complication of many treatments used in hematologic malignancies, affecting most patients whose neoplasms are treated with intensive chemotherapy, and virtually all those receiving myeloablative conditioning regimens prior to hematopoietic stem cell transplantation. Mucositis has been identified as a critical risk factor for infections and is a maj...

2017
Severine Cao Vinod E. Nambudiri

Anaplastic lymphoma kinase (ALK) is a receptor tyrosine kinase that has been implicated in the pathogenesis of a variety of neoplasms. As suggested by its name, ALK was first described as part of a translocation product in cases of anaplastic large-cell lymphoma, with other genetic and cytogenetic ALK mutations subsequently coming to attention in the development of many other hematologic and so...

Journal: :Haematologica 2012
Krisstina Gowin Prakash Thapaliya Jan Samuelson Claire Harrison Deepti Radia Bjorn Andreasson John Mascarenhas Alessandro Rambaldi Tiziano Barbui Catherine J Rea John Camoriano Amy Gentry Jean-Jacques Kiladjian Casey O'Connell Ruben Mesa

The Philadelphia negative myeloproliferative neoplasms, including polycythemia vera, essential thrombocythemia, and myelofibrosis, are associated with substantial vascular and transformative complications. Standard therapy for high-risk disease, particularly in patients that have failed initial therapy, remains controversial. Non-pegylated interferon has previously been shown to be effective in...

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