A case of hemifacial hyperplasia that presented with muscular, skeletal, and dental hyperplasia along with lipomatous infiltration was described. Advanced imaging was useful in identifying the lipomatous infiltration present in the lesion, which raises the possibility of lipomatosis having a diverse presentation in hemifacial hyperplasia. As there was a scarcity of related literature in the fie...

We report two cases of epidermal nevus syndrome (ENS) involving the spine. MR imaging of the spine demonstrated intraspinal lipomas in both cases. Abnormal, enhancing, enlarged cervical and lumbosacral nerve roots were present in one patient. Spinal imaging for patients with ENS may help in the diagnosis of subtle intracranial manifestations, as it did in both of our cases. ENS has features sim...

© 2009 The Authors. doi: 10.2340/00015555-0674 Journal Compilation © 2009 Acta Dermato-Venereologica. ISSN 0001-5555 Sir, Benign symmetric lipomatosis is a rare form of multiple, symmetrical fat distribution. The disorder was first described by Brodie in 1846. It was subsequently characterized by Madelung in 1888 and Launois & Bensaude in 1898 (for review see ref 1). Histologically, cells in th...

ring predominantly in the kidney. Extrarenal AMLs are rare, and those occurring in the retroperitoneal perinephric space are extremely rare, with only 13 previously reported cases (1-3). An AML in the perinephric space is a fat-containing tumor and is difficult to differentiate from other fatty lesions including lipomatosis, lipoma, and liposarcoma. We report a case of AML of the perinephric sp...