OBJECTIVE To report the clinical findings and management of spontaneous hemorrhage in an unsuspected intraorbital arteriovenous malformation. DESIGN Interventional case report. METHODS Review of clinical findings, radiologic studies, and treatment of the patient. RESULTS A 75-year-old woman sought treatment for the rapid onset of severe proptosis. Orbital exploration of a "mass" imaged on...

Conjoined twins are an extremely rare congenital malformation without any known genetic predisposition. Omphalopagus twins are the second most common variety of conjoined twins and usually are joined at the umbilicus. We present omphalopagus conjoined twins demonstrated with true FISP (fast imaging with steady-state procession) and HASTE (half- Fourier acquisition single-shot turbo spin-echo) m...

Capillary malformation-arteriovenous malformation syndrome is a rare type of vascular malformation first described in 2003. It is an autosomal dominant inherited disorder that has been reported in association with heterozygous mutations in the RASA1 gene, which encodes the protein RASp21. The clinical picture is characterized by multiple small capillary malformations which are associated with e...

BACKGROUND/PURPOSE To report a case of congenital retinal macrovessel associated with cystoid macular edema and an ipsilateral intracranial venous malformation. METHODS Case report. RESULTS A 58-year-old woman with decreased vision was found to have a congenital retinal venous macrovessel associated with cystoid macular edema because of tributary venous occlusion. The patient underwent neur...

Klippel Trenaunay syndrome refers to a rare congenital anomaly which is characterized by capillary malformation, venous malformation and sometimes lymphatic malformation associated with overgrowth of a limb, with soft tissue hypertrophy and/or bony hypertrophy. The anomaly, if present, is present at birth and usually involves the lower limbs as well as portion of trunk, face, uppper limb or hea...