نتایج جستجو برای: marfan syndrome

تعداد نتایج: 622133  

2016
Moritz Rippe Julie De Backer Kerstin Kutsche Laura Muiño Mosquera Helke Schüler Meike Rybczynski Alexander M. Bernhardt Britta Keyser Mathias Hillebrand Thomas S. Mir Jürgen Berger Stefan Blankenberg Dietmar Koschyk Yskert von Kodolitsch

BACKGROUND Mitral valve prolapse syndrome (MVPS) and MASS phenotype (MASS) are Marfan-like syndromes that exhibit aortic dilatation and mitral valve prolapse. Unlike in Marfan syndrome (MFS), the presence of ectopia lentis and aortic aneurysm preclude diagnosis of MVPS and MASS. However, it is unclear whether aortic dilatation and mitral valve prolapse remain stable in MVPS or MASS or whether t...

Journal: :Thorax 1984
J R Wood D Bellamy A H Child K M Citron

Hospital case notes and chest radiographs of 100 patients with Marfan syndrome were investigated for evidence of pulmonary disease. The criteria for inclusion of details of a given patient in the study were the occurrence of Marfan abnormalities in at least two separate body systems (skeletal, cardiovascular, ocular) or in one body system where there was a family history of a classically affect...

2017
Rawa Arif Marcin Zaradzki Anca Remes Philipp Seppelt Reiner Kunze Hannes Schröder Simon Schwill Stephan M. Ensminger Peter N. Robinson Matthias Karck Oliver J. Müller Markus Hecker Andreas H. Wagner Klaus Kallenbach

Marfan syndrome is characterized by high expression of matrix metalloproteinases (MMPs) in aortic smooth muscle cells (AoSMCs) associated with medial elastolysis and aortic root aneurysm. We aimed to reduce aortic elastolysis through decrease of MMP expression with decoy oligodeoxynucleotides (dODNs) neutralizing the transcription factor activating factor-1 (AP-1). AP-1 abundance in nuclear ext...

2015
Marco Cattalini Raju Khubchandani Rolando Cimaz

Chronic or recurrent musculoskeletal pain is a common complaint in children. Among the most common causes for this problem are different conditions associated with hypermobility. Pediatricians and allied professionals should be well aware of the characteristics of the different syndromes associated with hypermobility and facilitate early recognition and appropriate management. In this review we...

Journal: :Journal of Asian Pacific Society of Cardiology 2022

A 52-year-old man with Marfan syndrome presented symptomatic torrential tricuspid regurgitation (TR). Transcatheter edge-to-edge repair was attempted but could not reduce the TR significantly due to wide coaptation gap. He underwent transcatheter bicaval valve implantation TricValve device and this resulted in first successful of its kind Singapore.

Journal: :Ultrasound in Obstetrics and Gynecology 2007

Journal: :Interactive CardioVascular and Thoracic Surgery 2014

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