Histopathological studies on the cerebral aneurysm in cerebrovascular moyamoya disease have been limited to only a few cases and the pathological details still remain obscure. Six moyamoya disease autopsy cases that satisfied the criteria of this disease proposed by Nishimoto in 1976 are studied. In addition to the routine neuropathological examination of the brains, detailed observa tion of th...

OBJECTIVE Moyamoya disease is a cerebrovascular disorder characterized by progressive occlusion of vessels comprising the circle of Willis, resulting in formation of collaterals that have a cloudy appearance on angiography. Neuropsychological research on the cognitive effects of the disorder in adults has been limited in scope and generalizability; only a few case studies have been published. T...

Objective Moyamoya vasculopathy associated with skull base tumors has been rarely reported except for partially removed pituitary adenoma and craniopharyngioma. Only a single case of meningioma resulted in vast cerebral infarction. Surgical treatment carries a high risk of damage to the compensatory collateral circulation through leptomeningeal anastomosis leading to a devastating outcome. Case...

The authors present a rare case of moyamoya disease emerged with corpus callosum hemorrhage. A 31-year-old woman suddenly complained of severe headache followed by consciousness disturbance. Radiological examinations revealed the bleeding in the splenium of corpus callosum, which was associated with intraventricular hemorrhage. On cerebral angiography, the carotid fork was severely stenotic on ...

Superficial temporal artery-middle cerebral artery (STA-MCA) has been used for the treatment of occlusive cerebrovascular disease including moyamoya disease. The effect of STA-MCA bypass depends not only on the patency of anastomosis, but also on integrity and functional capacity of the donor artery. In the present prospective study, we investigated the effect of extensive stripping STA adventi...

Moyamoya disease can be associated with a rapidly progressive course in young patients. This report describes a patient with moyamoya disease who experienced rapid disease progression, resulting in cerebral infarction and a wide area of diminished cerebral perfusion. Double superficial temporal artery (STA)-middle cerebral artery (MCA) anastomoses were utilized to immediately increase cerebral ...

BACKGROUND AND PURPOSE Moyamoya disease is an idiopathic occlusive cerebrovascular disorder with abnormal microvascular proliferation. We investigated the clinical utility of leptomeningeal high signal intensity (ivy sign) sometimes seen on fluid-attenuated inversion recovery images in Moyamoya disease. MATERIALS AND METHODS We examined the relationship between the degree of the ivy sign and ...

Moyamoya disease is a disease of the cerebral vessels, which is characterized by narrowing of the intracranial vessels as they emerge from the base of the skull, and hypertrophy of fine collateral vessels in response to this vessel narrowing. Moyamoya means the puff of smoke in Japanese, and refers to the appearance of the abnormal fine collateral vessels appearing on cerebral angiography in pa...