INTRODUCTION Chronic post-anoxic myoclonus, also known as Lance-Adams syndrome, may develop following hypoxic brain injury, and is resistant to pharmacological therapy. CASE REPORT The patient we presented developed post-anoxic action myoclonus with severe, completely incapacitating myoclonic jerks. Myoclonus did not respond to the treatment with commonly used agents, i.e. valproate and clona...

BACKGROUND Various movement disorders can be found in ataxia-telangiectasia (AT), including ataxia, dystonia, chorea, and myoclonus, but myoclonus has rarely been described as the predominant feature in AT. CASE REPORT We report two AT patients with prominent myoclonus, illustrating an unusual presentation of this disorder. Sequencing of the ATM gene in the first patient revealed a homozygous...

=Abstract=Sprague-Dawley rat fetuses ranging from 15to 19-day of gestational age, were studied with their rugae morphogenesis a t the light microscopic level. The distribution of collagen fibers in the palatal mesenchyme was analyzed. In addition, an attempt to evaluate the role of collagen fibers in rugae development was made. The specimens were H-E stained and collagen fiber stained according...

It is widely acknowledged that in some forensic situations there are limitations to identification of the deceased by fingerprints, DNA and dental records. Palatal rugae pattern of an individual may be considered as a useful adjunct for sex determination for identification purposes. The aim of this study was to identify and compare the rugae pattern in Indian males and females, as an additional...

Any attentive observer of families who have a child afflicted with a cleft lip whether or not associated with a palatal cleft would be certain to be impressed by the importance of the psychological context of their interpersonal exchanges and the risks of a breakdown in the parent-child relationship adversely affecting the child’s development. The birth of a child with a cleft lip inevitably be...

During secondary palate development, palatal shelves adhere to each other in the midline to form a midline epithelial seam leading to palatal closure. Cell-cell and cell-extracellular matrix adhesions, which are mediated by cell adhesion receptors, E-cadherin and integrins, are implicated in the process of adhesion of the palatal shelves. Src family kinases (SFK) function downstream of both rec...

introdouction: variations in root canal morphology pose a challenge for successful endodontic treatment. the root canal anatomy of the maxillary first molar has been often described as three roots with four canals (two mesiobuccal, one distobuccal, and one palatal). the occurrence of two palatal canals in one palatal root is quite rare. this report represents the case of a maxillary first molar...

BACKGROUND The maxillary swing procedure has been used as an anterolateral approach to expose the nasopharynx, the central skull base, and its vicinity. The reported incidence of postoperative palatal fistula has ranged from 20% to 25%. The oronasal incompetence especially associated with a large fistula has adversely affected normal speech, eating, and swallowing functions. We describe a modif...

To evaluate cellular immune activation in opsoclonus-myoclonus syndrome, we measured the inflammatory marker neopterin in the cerebrospinal fluid of 16 children with opsoclonus-myoclonus and neuroblastoma, 24 children with opsoclonus-myoclonus but no tumor, and 19 age-matched controls. The mean concentration in opsoclonus-myoclonus was 2.3-fold higher than in controls (P = .008). Neopterin was ...

Cortical tremor (CT) is a form of cortical reflex myoclonus that can mimic essential tremor (ET). Clinical features that are helpful in distinguishing CT from ET are the irregular and jerky appearance of the movements. We report two patients with CT with coexisting orthostatic movements, either orthostatic tremor (OT) or myoclonus, who experienced functional improvement in both cortical myoclon...