نتایج جستجو برای: proteins deficiency

تعداد نتایج: 681154  

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2016
Andrew G Cox Allison Tsomides Andrew J Kim Diane Saunders Katie L Hwang Kimberley J Evason Jerry Heidel Kristin K Brown Min Yuan Evan C Lien Byung Cheon Lee Sahar Nissim Bryan Dickinson Sagar Chhangawala Christopher J Chang John M Asara Yariv Houvras Vadim N Gladyshev Wolfram Goessling

Selenium, an essential micronutrient known for its cancer prevention properties, is incorporated into a class of selenocysteine-containing proteins (selenoproteins). Selenoprotein H (SepH) is a recently identified nucleolar oxidoreductase whose function is not well understood. Here we report that seph is an essential gene regulating organ development in zebrafish. Metabolite profiling by target...

Journal: :Molecular aspects of medicine 2004
Jean-Paul Bonnefont Fatima Djouadi Carina Prip-Buus Stephanie Gobin Arnold Munnich Jean Bastin

Carnitine palmitoyltransferase (CPT) deficiencies are common disorders of mitochondrial fatty acid oxidation. The CPT system is made up of two separate proteins located in the outer (CPT1) and inner (CPT2) mitochondrial membranes. While CPT2 is an ubiquitous protein, three tissue-specific CPT1 isoforms--the so-called "liver" (CPT1-A), "muscle" (CPT1B) and <> (CPT1-C) CPT1s--have been sho...

2016
Meizhen Li Xinguo Shi Chentao Guo Senjie Lin

Phosphorus (P) is an essential nutrient element for the growth of phytoplankton. How P deficiency affects population growth and the cell division cycle in dinoflagellates has only been studied in some species, and how it affects photosynthesis and cell growth remains poorly understood. In the present study, we investigated the impact of P deficiency on the cell division cycle, the abundance of ...

2011
Youngeun Ma Eui-Hoon Kwon Jung-Eun Lee Kihyun Kim Hee-Jin Kim Sun-Hee Kim

Amyloidosis is a heterogeneous group of diseases in which misfolding of extracellular proteins is the pathogenic factor. Light chain amyloidosis (AL) is the most common form of amyloidosis, and the causative proteins in AL are the immunoglobulin light chains produced by clonal plasma cells. Hemorrhagic events, ranging from mild subcutaneous hemorrhage to life-threatening bleeding, account for a...

2009
RAMEZAN ALI KHAVARI-NEJAD FARZANEH NAJAFI

Tomato plants were grown hydroponically under different deficient regimes of nitrogen (N) and phosphorus (P) in the form of nitrate and phosphate. Results showed a severe reduction in growth, soluble protein and chlorophylls contents under N deficiency, which suggested accelerating of leaf senescence. Furthermore, it was accompanied by enhanced activity of peroxidase and sugars contents that we...

Journal: :The British journal of nutrition 2004
John H Beattie In-Sook Kwun

The development of atherosclerosis is influenced by genetic, lifestyle and nutritional risk factors. Zn and metallothionein deficiency can enhance oxidative-stress-related signalling processes in endothelial cells, and since changes in available plasma Zn may affect the Zn status of the endothelium, Zn deficiency could be a risk factor for IHD. Although the association of Zn with many proteins ...

Journal: :The Journal of biological chemistry 2007
Bingzhong Xue Young-Bum Kim Anna Lee Elena Toschi Susan Bonner-Weir C Ronald Kahn Benjamin G Neel Barbara B Kahn

Mice heterozygous for insulin receptor (IR) and IR substrate (IRS)-1 deficiency provide a model of polygenic type 2 diabetes in which early-onset, genetically programmed insulin resistance leads to diabetes. Protein-tyrosine phosphatase 1B (PTP1B) dephosphorylates tyrosine residues in IR and possibly IRS proteins, thereby inhibiting insulin signaling. Mice lacking PTP1B are lean and have increa...

Journal: :The Journal of neuroscience : the official journal of the Society for Neuroscience 2015
Fu-Lei Tang Joanna R Erion Yun Tian Wei Liu Dong-Min Yin Jian Ye Baisha Tang Lin Mei Wen-Cheng Xiong

Vacuolar protein sorting-35 (VPS35) is essential for endosome-to-Golgi retrieval of membrane proteins. Mutations in the VPS35 gene have been identified in patients with autosomal dominant PD. However, it remains poorly understood if and how VPS35 deficiency or mutation contributes to PD pathogenesis. Here we provide evidence that links VPS35 deficiency to PD-like neuropathology. VPS35 was expre...

Journal: :The Proceedings of the Nutrition Society 2001
W Burke G Imperatore M Reyes

Like most essential nutrients, Fe needs to be maintained in the body at a defined level for optimal health, with appropriate adaptation to varying Fe needs and supply. The primary mechanism for controlling Fe level is the regulation of Fe absorption. Several different proteins have been identified as contributors to the process. Despite a complex regulatory system, Fe disorders (both Fe deficie...

Journal: :Archives of disease in childhood 1986
M E McGraw D A Price D J Hill

Two sisters of Asian origin showed typical clinical and biochemical features of primary somatomedin C (SM-C) deficiency (Laron dwarfism). Abnormalities of SM-C binding proteins were observed, one sister lacking the high molecular weight (150 Kd) protein.

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