Objective: One and one half ventricle repair is a surgical option for congenital cardiac anomalies characterised by right ventricle (RV) hypoplasia and/or dysplasia. Methods: From March 1994 to March 2001, eight patients (mean age 9.1 years, range 7 months to 35 years) with hypoplastic and/or dysplastic RV underwent correction of their intracardiac anomaly in association with a BCPS (one and on...

Double-chambered right ventricle (DCRV) is an uncommon congenital heart disease. Anomalous muscle bundles in the right ventricle divide the right ventricle into two portions and cause intracavitary obstruction of the right ventricle. We report a patient with DCRV mimicking asymmetric septal hypertrophy. We did clinical, echocardiographic and angiographic evaluation. Surgical intervention was su...

To cite: Mathew JJ, Hollings NP, Myers JD. Thorax 2013;68:796–797. An 18-year-old female subject with a history of decortication for right sided, postpneumonic pleural thickening presented with haemoptysis. A CT pulmonary angiogram showed marked hypoplasia of the right main, lobar and segmental pulmonary arteries, along with reduced volume of the right lung. Prominent bronchial artery supply to...

The catastrophic consequences for patients in the settings of certain clinical conditions such as acute right ventricular infarction or massive pulmonary embolism with right heart failure illustrate the essential role that the right ventricle plays in sustaining life. With the development of more sophisticated diagnostic imaging technologies at the end of the last century and the dawn of this c...

A PediaSat™ oximetry catheter (PediaSat: Edwards Lifesciences Co., Ltd., Irvine, CA, U. S. A.), which facilitates continuous measurement of central venous oxygen saturation (ScvO2), may be useful for surgery for pediatric congenital heart disease. We used PediaSat during a bidirectional Glenn shunt. The patient was a 13-month-old boy. Under a diagnosis of left single ventricle (pulmonary atresi...

THE DIVISION of the right ventricle into two chambers by aberrant, hypertrophied muscular bands is a relatively rare congenital cardiac malformation. No reports have been found that describe the details of anatomic structure and hemodynamics in this anomaly, although Keith, Rowe, and Vlad' and Kjellberg et al.2 alluded to this malformation in their texts. Grant, Downey, and MacMahon3 described ...

Aplasia of condyle is very rare, when this condition not seen as a part of a syndrome. We report a case of condylar aplasia on the right side and hypoplasia on the left side in a 21-year-old female. The patient reported to the department with a chief complaint of underdeveloped lower jaw. Clinical examination, conventional radiographs, and 3D CBCT images revealed complete absence of condyle on ...