INTRODUCTION Poland syndrome is a congenital disorder related to chest and hand anomalies on one side of the body. Its etiology remains unclear, with an ipsilateral vascular alteration (of unknown origin) to the subclavian artery in early embryogenesis being the currently accepted theory. Cavernous malformations are vascular hamartomas, which have been linked to a genetic etiology, particularly...

Congenital extra hepatic port systemic shunt, is a rare clinical entity which can lead to hepatopulmonary syndrome wherein blood from portal vein directly drains into circulation, causing an alteration in metabolism of pulmonary vasoactive substances, vasodilatation, diffusion-perfusion defects, and eventually, arterial hypoxemia due either increase vascular resistance or the creation arteriove...

Purpose: Arteriovenous malformations (AVM) of the head and neck are rare anomalies, but often present with significant haemorrhage or cosmetic defects. The purpose of this study is to determine the effectiveness of embolization of each type of vascular malformation. Methods: A retrospective review was performed between January 2009 to June 2015 on 36 patients who were diagnosed vascular malform...

BACKGROUND Dural sinus malformation (DSM) is a term used to describe congenital vascular malformations characterized by massive dilation of one or more dural sinuses: these dilatations are typically associated with arteriovenous shunts. Such malformations can present antenatally but their early natural history and anatomy is poorly defined. METHODS We reviewed five years of autopsy experience...

Vascular malformations are anomalies always present at birth that, contrary to hemangiomas, never regress and may grow during lifetime. Clinical presentation of vascular malformations is extremely variable and ranges from asymptomatic spots of mere aesthetic concern to lesions with high blood flow or located in critical sites that may be life-threatening. Given the low incidence of these disord...

F acial vascular malformations can cause dental emergencies that result in fatal or life-threatening and disfiguring situations. 14 Dentists must be aware of the clinical manifestations of these lesions in order to prevent iatrogenically related accidents and to minimize potential spontaneous crises for the patient. Effective treatment depends on the type and location of vascular lesion. Litera...

Vascular anomalies are congenital vascular tissue aberrations, hich are commonly identified in the head and neck and known to ffect approximately 1 in 22 children. The most recent classificaion of vascular anomalies includes two main categories: vascular umours (haemangiomas) and vascular malformations [1]. Several problems can arise from vascular tumours, including unctional (through mass effe...

A role for the Notch signalling pathway in the formation of arteriovenous malformations during development has been suggested. However, whether Notch signalling is involved in brain arteriovenous malformations in humans remains unclear. Here, we performed immunohistochemistry on surgically resected brain arteriovenous malformations and found that, compared with control brain vascular tissue, No...

OBJECT Onyx-18 is a relatively new liquid embolic agent. The initial success with this polymer will result in increased utilization in children, but its use and safety in the pediatric population have not been firmly established. METHODS Between December 2005 and January 2008, the cerebral vascular malformations in 6 children were embolized using Onyx-18. The ages of the patients ranged from ...