anomalous origin of the left coronary artery from the pulmonary artery (alcapa) is a rare congenital cardiac malformation. we report three cases of alcapa who survived to adulthood. the first case was a 51-year-old woman who complained of typical chest pain that was diagnosed with alcapa using cardiac catheterization and coronary computed tomographic angiography (cta). the second case was a 30-...

the purpose of this study was to evaluate the early and late outcome after total correction of tetralogy of fallot (tof) in 101 consecutive patients with a mean age of 8.23 ± 4.90 years underwent repair of surgery at one institution between 1995 and 2006. forty two patients had initial palliative operations. a transannular patch was inserted in 60 (58.5%) patients. risk factors for operative mo...

background and objective: congenital heart disease (chd) is the most form of cardiovascular disease in children. chd have different presentations, from defects that progress asymptomatically to those with significant symptoms and high mortality. this study was performed to highlight the importance of signs and symptoms to diagnosis of chd neonates. materials & methods: this descriptive an...

conclusions in the children in this study, pacemaker accelerometers failed to meet physiological demands. results basal heart rates, maximal heart rates, and exercise tolerance were significantly lower in the children with pacemakers. age, sex, and body mass index had no effect on the heart rate slope during the exercise test. there was no significant difference between epicardial and endocardi...

normal 0 false false false en-us x-none fa background : fahr's disease is a rare neurodegenerative disorder of unknown cause characterized by idiopathic basal ganglia calcification that is associated with neuropsychiatric and cognitive impairment. no case of fahr's disease with associated cardiac conduction disease has been described in the literature to date. the objective of this case report ...

BackgroundCongenital heart diseases (CHD) are the most common congenital anomaly in children and also the leading cause of mortality from congenital anomalies. Various factors including smoking, drinking alcohol and addiction play role in development of congenital heart diseases. This study was conducted with the aim of investigation of the prevalence of addiction in parents of children with co...

the most common congenital diseases in children is congenital heart disease. factors such as environment, genetic, old maternal age during pregnancy, maternal disease and using medicine in pregnancy, prematuritiy, and specific seasons are significant in the prevalence of disease.materials and methods: a cross sectional study was conducted to investigate the status of children with congenital he...

Noonan Syndrome (NS) is an autosomal dominant disorder in which parents with syndrome have a 50percent chance of passing the mutation to their children, most commonly due PTPN11 gene. In clinical case, we identified male child who showed features such as short stature, congenital heart disease and peculiar facial appearance, strongly suspecting syndrome. The purpose this article report presenta...

a total of 14 cases of infective endocarditis (ie) in children aged 6 months to 10 years were seen from december 1987 to december 1992 at the pediatric unit of ayatollah taleghani medical center. the majority of patients (12 of 14) were between 5 and 10 years of age. acyanotic congenital heart disease was known to preexist in 78.6% and rheumatic valvular heart disease in 21.4% of cases. organis...

Alagille Syndrome (ALGS) is a rare autosomal dominant disorder that affects multiple organ systems. Cholestasis as a result of a paucity of intrahepatic bile ducts and congenital heart defects are the two most common features of ALGS. We describe a case of ALGS with novel mutations of JAG1 and NOTCH2 genes in a newborn girl with complex congenital heart disease, bilateral dysplastic kidneys, an...