INTRODUCTION Congenital lobar emphysema (CLE) and Williams-Beuren Syndrome are two rare conditions that have only been reported together in a single case study. CASE PRESENTATION We report another case of a male Caucasian newborn with nonspecific initial respiratory distress, with detection of CLE on repeat chest X-ray on Day 25 of life and concurrent ventricular septal defect, supravalvular ...

Congenital lobar emphysema is a rare disorder thay may present outside the newborn period. It is generally best treated surgically by excision of the affected lobe. We describe a 6 1/2-week-old infant in whom the initial auscultatory and roentgenographic findings were confusing and of no help in making the diagnosis. The etiology of congenital lobar emphysema remains unclear.

Massive lobar emphysema in the middle lobe of the right lung was observed in a dog brought to our clinic with sudden onset of tension pneumothorax, and lobectomy was performed to excise it. Pathological examination resulted in a diagnosis of congenital bronchiectasis associated with bronchial cartilage hypoplasia. Two cases of diagnosis and successful treatment of congenital lobar emphysema hav...

Congenital lobar emphysema (CLE) is an uncommon congenital malformation of the lung that can present with respiratory distress in early life. We report a full term female baby who presented with intermittent bluish discoloration of the lips and extremities during crying since birth. An initial diagnosis of left sided collapse-consolidation with right-sided compensatory emphysema was made from c...

Congenital lobar emphysema (CLE) is a cause of respiratory distress in newborns and infants. In this study we presented a complicated case of CLE in a 35-day-old infant who was treated successfully with surgical intervention. We reviewed several articles and texts to offer a complete discussion about clinical and paraclinical aspects of this entity. (Tanaffos 2003; 2(5):

Giant congenital lobar emphysema is a rare pathological malformation in infants. Authors report a similar case that is remarkable for its even rarer segmental location and compressive character. The patient underwent successful urgent segmentectomy for the treatment of respiratory distress in a developing country.

There is a broad spectrum of bronchopulmonary malformations which present in early infancy and childhood. These include Bronchogenic cysts, Bronchopulmonary sequestrations, congenital cystic adenomatoid malformation (CCAM), and congenital lobar emphysema. These lesions maybe detected by prenatal diagnosis, present as acute respiratory distress in the newborn period, or may remain undiagnosed an...