Congenital cystic adenomatoid malformation is a rare, but well-known disease. It can be managed conservatively in patients without symptoms or require surgical removal when symptomatic. The surgical option of choice is en bloc resection of the affected lesion. We report an experience of life-threatening congenital cystic adenoid malformation in a low-birth-weight (1,590 g) premature neonate who...

Congenital cystic adenomatoid malformation of the bronchi with bilateral lung involvement has only previously been reported in one possible adult case. This report describes a young man with bilateral diffuse lung involvement, characteristic histological features, and a mixed restrictive/obstructive lung function pattern.

In recent years the diagnosis of congenital cystic disease of the lung has been clarified and restricted as a result of the recognition of a variety of emphysematous and cystic lesions of diverse etiologies. True cystic disease is rare.1 Rarer still is the closely related condition first reported in 1897 by Stoerk as " cystic fetal bronchial adenoma, " 2 and introduced in the English language m...

Congenital cystic adenomatoid malformation (CCAM) of the lung is an uncommon congenital anomaly, especially in young adults. This study reports an 18-yr-old male with CCAM involving the right upper lobe, who presented with a moderate spontaneous haemopneumothorax initially. The patient also had bilateral abdominal cryptorchidism which required surgical treatment earlier in childhood. The chest ...

Congenital lung lesions that can be diagnosed on the basis of prenatal sonography include cystic adenomatoid malformations and extrapulmonary bronchopulmonary sequestrations. Intralobar bronchopulmonary sequestration is a rare congenital malformation of the lung. The prenatal sonographic features of this condition are reported here.

OBJECTIVE To review the management and outcome of babies with antenatally diagnosed congenital cystic adenomatoid malformation. DESIGN Retrospective cohort review. SETTING Tertiary neonatal care unit at Queen Mary Hospital and antenatal diagnostic centre at Tsan Yuk Hospital. PATIENTS Consecutive patients with antenatally suspected congenital cystic adenomatoid malformation in their conce...

Congenital cystic adenomatoid malformation (CCAM) is a rare pulmonary malformation resulting from excessive overgrowth of the terminal bronchioles. We present two CCAM case studies: type I (macrocystic) and type III (microcystic), diagnosed by antenatal ultrasonography at 31 and 21 weeks' gestation, respectively. In the former, multiple dilated cystic masses in the fetal left lung, with polyhyd...

Congenital lung abnormalities are relatively rare but very dangerous for the fetus and neonate. This article describes the most common pulmonary complications observed during pregnancy such as congenital cystic adenomatoid malformation, diaphragmatic hernia, bronchopulmonary sequestration, hydrothorax, chylothorax, lung agenesia, pulmonary hypoplasia. The diagnostic methods and available therap...