A 41-year-old woman presented with a 2-year history of multiple asymptomatic pea-sized papules with an erythematous, telangiectatic rim surrounding an atrophic, porcelain-white center on the trunk and extremities (Figure 1). She had experienced abdominal fullness and vomiting for 1 year. Histopathologic examination of a skin biopsy from the left forearm revealed hyperkeratosis, epidermal atroph...

BACKGROUND Degos disease is a very rare syndrome with a rare type of multisystem vasculopathy of unknown cause that affects the skin, gastrointestinal tract, and central nervous system. Other organs such as the kidneys, lungs, pleura, liver, heart, and eyes, can also be involved. OBJECTIVE To highlight the incidence of Degos disease with regard to age and sex, discuss the necessity of its acc...

Galli-Galli disease is a rare acantholytic variant of Dowling-Degos disease, with few cases reported in the literature. We describe a case of Galli-Galli disease and review the literature.

Vol. 27, No. 2, 2015 235 Received March 13, 2014, Revised May 14, 2014, Accepted for publication June 23, 2014 Corresponding author: Jee-Bum Lee, Department of Dermatology, Chonnam National University Hospital, 42 Jebong-ro, Dong-gu, Gwangju 501-757, Korea. Tel: 82-62-220-6684, Fax: 82-62-222-4058, E-mail: [email protected] This is an Open Access article distributed under the terms of the Creati...

Degos-like lesions (DLL) have been associated with connective tissue diseases. Till date only twelve cases of systemic lupus erythematosus (SLE) DLL published. We describe a rare case SLE leg ulcers and DLL. A 23-year-old male presented malar rash, photosensitivity, ulcers, joint pain, oral altered sensorium dyspnea. Cutaneous examination also revealed atrophic, porcelain-white scars over body ...

Degos' disease, or malignant atrophic papulosis, is a rare and often fatal multisystem vasculopathy of unknown etiology. The cutaneous manifestations comprise erythematous papules, which heal to leave scars with a pathognomonic central porcelain-white atrophic area and a peripheral telangiectatic rim. Involvement of the gastrointestinal tract is observed in 50% of cases, with intestinal perfora...

Galli- Galli disease is a rare acantholytic variant of Dowling- Degos disease, with few cases reported in the literature till date. We here, describe an interesting case prominent histopathological findings. Future studies and genotype-phenotype correlations may elucidate why acantholysis observed some patients, but not others.

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