Although craniofacial bone is the second common site of fibrous dysplasia involvement, it is rarely found in the paranasal sinus. Among fibrous dysplasia of the head and neck, the maxilla and mandible are the most frequent sites to be involved. Fibrous dysplasia becomes dormant in adolescence and early adult life and is more common in female. It is one of the fibrous osseous lesions and should ...

BACKGROUND Fibrous dysplasia is a rare bone disorder, commonly associated with pain, deformity and fractures, which may significantly impact on quality of life. In this study we evaluate quality of life in patients with fibrous dysplasia using the Short Form-36 and the Brief Pain Inventory questionnaires. Data were compared with those of the general Dutch population. RESULTS Out of 138 patien...

Dr. Raphael Vicente Alves – Rua Estado de Israel 907 / 31 04022-002 São Paulo SP Brasil. E-mail: [email protected] Co-existing fibrous dysplasia and meningothelial meningioma is extremely rare. A search at “PubMed” (U.S. National Library of Medicine) with terms “fibrous”, “dysplasia” and “meningioma” demonstrated a total of 7 cases reported. Three cases in association with McCune-Albri...

Since Coley and Stewart (1945) recorded two cases of sarcomatous change in polyostotic fibrous dysplasia, there have been a further twelve reported cases ofmalignant change occurring in patients with fibrous dysplasia (Table I). Eight ofthese occurred in patients with polyostotic fibrous dysplasia and, of these, three were in patients with Albright’s syndrome. Of the other six patients, in five...

Clinical, endocrinological and computed tomographic features of three patients with unusual manifestations or complications of craniofacial involvement of fibrous dysplasia are presented. One patient with polyostotic fibrous dysplasia presented in late pregnancy with acute onset of bilateral optic nerve compression and blindness secondary to a rapidly expanding mass of fibrous dysplasia tissue ...

normal bone marrow is replaced with fibro-osseous tissue. Patients are often asymptomatic, and fibrous dysplasia is often detected incidentally in patients with malignancy in whom F-fluoro-2deoxy-glucose positron emission tomography (F -FDG PET/ CT) is performed for metastatic disease. PET/CT findings of fibrous dysplasia have been reported on several papers. The level of FDG uptake in fibrous ...

Fibrous dysplasia is a benign fibrous-osseous lesion in which normal bone is replaced by fibrous connective tissue and immature bone, affecting only one (monostotic) or several bones (polyostotic) and mainly occurring in children and young adults. When present in facial bones, the maxilla is more frequently involved than the mandible, which can cause facial asymmetry in addition to dental compl...

AIM Fibrous dysplasia is a benign disease in which medullary bone is replaced by fibro-osseous tissue, and causes distortion and overgrowth of the involved bone and represents about 3% of all bone tumors. There is variability in the manifestation of Fibrous Dysplasia lesions with imaging techniques due to their proportional variations of fibrous to osseous tissue. Radiological d...

INTRODUCTION First described by Von Recklinghausen in 1891, fibrous dysplasia is a developmental defect of osseous tissue such that bone is produced with an abnormally thin cortex and marrow is replaced with fibrous tissue that demonstrates characteristic ground-glass appearance on x-ray examination. The underlying defect in fibrous dysplasia is a mutation of the GNAS1 gene, which leads to cons...