Hypoplastic left heart syndrome is a rare critical congenital defect constituting prevalence of 1/3,500 to 1/12,500 live births in which there obstructions the blood flow within heart. Here we present case full-term 38 weeks male baby with birth weight 3.5 kg, and no obvious physical deformity referred our centre at 22 hours life for respiratory distress cyanosis. At 23 life, he was diagnosed h...