E10 CUTIS WWW.CUTIS.COM To the Editor: Nevus of Ota, also known as oculodermal melanocytosis or nevus fuscoceruleus ophthalmomaxillaris, is a hamartoma of dermal melanocytes that is characterized by a unilateral or bilateral blue-brown, speckled patch usually involving the malar, periorbital, temple, and/or forehead regions of the face.1 It also may affect the sclera, conjunctiva, retinas, corn...

Phacomatosis pigmentovascularis is a rare, congenital condition characterized by a combination of cutaneous melanocytic lesions and vascular malformation. We discuss an entirely unique case of Phacomatosis pigmentovascularis with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita, which may represent a heretofore undescribed vari...

Oculodermal melanocytosis, also known as Nevus of Ota, is a hamartomatous melanocytic nevus of dermal melanocytes. It presents as a bluish grey patch on the face, which may be congenital or acquired involving the area of distribution of the ophthalmic and maxillary branches of the trigeminal nerve. The nevus can be unilateral or bilateral, and, in addition to skin, it may involve ocular and ora...

Nevus of Ota is a rare pigmented disorder affecting the skin along the distribution of trigeminal nerve. Oral involvement of this pigmented lesion is very rare. Classification of Nevus of Ota given by Tanino represents the skin manifestations well but does not include the extra cutaneous manifestations. Hence an addition to this classification is being proposed through this case report which de...

[This corrects the article on p. 446 in vol. 29, PMID: 28761293.].

We report phakomatosis pigmentovascularis (PPV) detected in a 40yearold male characterized by the presence of a port-wine stain in the background of aberrant Mongolian spots covering the back, nevus of Ota, ocular melanosis, epidermal nevus and a scaly patch with the diagnosis of discoid lupus erytematosus. These associations have not been reported yet.