نتایج جستجو برای: pyridoxine depended seizures

تعداد نتایج: 88326  

Journal: :Archives of disease in childhood 1984
K N Hansen J R Ostergaard S M Møller

Pyridoxine dependent seizures is a rare autosomal recessive disorder. Its manifestations are intractable epilepsy leading to death in status epilepticus. Treatment with pyridoxine prevents the seizures and normalizes the EEG. Early diagnosis is important for the intellectual outcome. In Denmark, the disease has occurred in a child of healthy Tamil immigrants, who are first cousins. The child's ...

Journal: :Archives of disease in childhood 2005
J V Been L A Bok P Andriessen W O Renier

BACKGROUND Pyridoxine dependent epilepsy is a rare cause of seizures in childhood. The diagnosis is made on clinical criteria, that in many cases are never met. Therefore, epidemiological data on pyridoxine dependency are scarce. AIMS To study the epidemiology of pyridoxine dependent epilepsy in the Netherlands, and to determine whether the diagnosis is based on the appropriate criteria. ME...

Journal: :Pediatric Neurology Briefs 1996

Journal: :Pediatric Neurology Briefs 1994

2014
Philippa B. Mills Stephane S.M. Camuzeaux Emma J. Footitt Kevin A. Mills Paul Gissen Laura Fisher Krishna B. Das Sophia M. Varadkar Sameer Zuberi Robert McWilliam Tommy Stödberg Barbara Plecko Matthias R. Baumgartner Oliver Maier Sophie Calvert Kate Riney Nicole I. Wolf John H. Livingston Pronab Bala Chantal F. Morel François Feillet Francesco Raimondi Ennio Del Giudice W. Kling Chong Matthew Pitt Peter T. Clayton

The first described patients with pyridox(am)ine 5'-phosphate oxidase deficiency all had neonatal onset seizures that did not respond to treatment with pyridoxine but responded to treatment with pyridoxal 5'-phosphate. Our data suggest, however, that the clinical spectrum of pyridox(am)ine 5'-phosphate oxidase deficiency is much broader than has been reported in the literature. Sequencing of th...

Journal: :Seizure 2007
L. K. Teune J. H. vd Hoeven N. M. Maurits A. F. Bos J.W.C. Alffenaar D. J. Reijngoud O. F. Brouwer D. A. Sival

PURPOSE In infants with frequent therapy resistant seizures (TRS-infants), clinical detection of pyridoxine-dependency (PD) or -responsiveness (PR) occurs by empirical intravenous (IV) pyridoxine administration during recording of the EEG. However, in undiagnosed TRS-infants it is still unclear to what extent EEG alterations by pyridoxine-IV are attributable to PD/PR or to non-specific response...

Journal: :Pediatric Neurology Briefs 1998

2010
Omid Yaghini Mohammad-Amir Shahkarami Somayeh Shamsaii Viroj Wiwanitki Sedigheh Ebrahimi Soheil Ashkani Esfahani Hamidreza Ghafarian Mahsima Khoshneviszade

Omid Yaghini, MD; Mohammad-Amir Shahkarami*, MD; Somayeh Shamsaii, MD Pediatrics Department, Isfahan University of Medical Sciences, Isfahan, IR Iran Received: Nov 02, 2009; Accepted: Mar 13, 2010 Vitamin B6 (pyridoxine) dependent seizure (PDS) is an autosomal-recessively inherited disorder which starts within a few hours of birth or even earlier, and can cause intrauterine seizures[1,2]. It oc...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید