To cite: Oylumlu M, Dogan A, Ercan S, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/ bcr-2013-202760 DESCRIPTION A 20-year-old man with no history of known cardiac disease was admitted with dyspnoea on exertion during a few weeks. His effort capacity was class I. At physical examination, his blood pressure was 120/ 70 mmHg and pulse 80 bpm. His physical exami...

= Abstract =An autopsy case is described of a premature closure of the foramen ovale with a marked dilatation of the left atrium and an intact ventricular septum with aortic atresia but without left ventricular hypoplasia. This 28-week-old male baby was a stillborn to a 34-year-old multiparous mother. An intrauterine sonogram revealed marked ascites with anasarca, an enlarged left atrium and ve...

This is a case report of an 8-month-old infant with congenital heart disease including; pulmonary atresia, intact ventricular septum, right ventricular hypoplasia, atrial septal defect, coronary sinusoids (fistulas between right ventricle and left anterior descending artery). The patient had a stent for patent ductus arteriosus at 3 months of age and after 4 months a bidirectional Glenn shunt o...

Two cases are reported of truncus arteriosus communis arising entirely from the right ventricle and associated with interruption in one case and tubular hypoplasia of the aortic arch in the other. A haemodynamic hypothesis of preferential blood flow is proposed to explain this rare association.

A 2-month-old patient with transposition of the great arteries, a ventricular septal defect, pulmonary stenosis, and severe hypoplasia of the right ventricle successfully underwent a biventricular repair utilizing the aortic translocation technique. Advantages of this surgical repair over the Rastelli procedure in the management of this complex congenital heart lesion are discussed.

The "Scimitar syndrome" is a rare congenital anomaly characterized by combination of partial or complete pulmonary venous return from the right lung to the inferior vena cava either above or below the diaphragm together with hypoplasia of the right lung and sometimes systemic arterial supply to the right lung. In this case, multimodality imaging findings such as the vein draining into the infer...

Correlative angiographic-anatomical studies in 19 cases of pulmonary atresia with intact ventricular septum showed the following relations between the angiographic appearance of the pulmonary valve and the morphology of the right ventricle. (1) Doming of the pulmonary valve was associated with a nearly normal-sized right ventricle and a wide infundibulum patent to the level of the pulmonary val...

Correlative angiographic-anatomical studies in 19 cases of pulmonary atresia with infarct ventricular septum showed the following relations between the angiographic appearance of the pulmonary valve and the morphology of the right ventricle. (1) Doming of the pulmonary valve was associated with a nearly normal-sized right ventricle and a wide infundibulum patent to the level of the pulmonary va...

Left ventricular isolated hypoplasia is a seldom-described cardiac abnormality. Right usually associated with congenital anomalies of the pulmonary or tricuspid valve, whereas biventricular apical has never been described. We report case 48-year-old man no history known disease who was found to have complex abnormality characterized by: 1) Deficiency myocardium within apex adipose tissue infilt...

OBJECTIVE To assess the efficacy of arterial duct angioplasty in maintaining adequate ductal patency in neonates with critical pulmonary valve stenosis. PATIENTS Two neonates presenting with cyanosis due to critical pulmonary valve stenosis with severe right ventricular hypoplasia underwent percutaneous balloon dilatation of the pulmonary valve. Despite successful dilatation, both remained cy...