critical pulmonary valve stenosis (cpvs) and atrial septal defect (asd) is an uncommon form of congenital heart disease. concurrent transcatheter pulmonary valvuplasty and closure of secundum atrial septal defect appears to be an interesting alternative to surgical correction. we present the simultaneous balloon valvuloplasty of critical pulmonary stenosis (ps) with supra systemic right ventric...

  Cor triatriatum is an acyanotic congenital heart disease. We present a rare case of cor triatriatum sinistrum in a 6-month-old female infant who was presented with cyanosis and failure to thrive. The 2D transthoracic echocardiography and the Doppler color flow imaging showed a proximal venous chamber communicating to the distal left atrium  through restrictive opening to the low-pressure, dis...

one of the complications of twinning of mono chorionic mono amniotic gestations is conjointed twins. structural congenital malformations occur in 5 % to 7 % of twin gestations versus only 3 % of singleton births. most defects occurring in only one of the twin fetuses. occasional anomalies such as omphalocele sincenomalia heart defect one reported in both concordance. the structural defect commo...

BACKGROUND Atrial septal defect often become more severe when encountered in genetic syndromes. Congenital disorder of glycosylation type 1a is an inherited metabolic disorder associated with mutations in PMM2 gene and can affect almost all organs. Cardiac abnormalities vary greatly in congenital disorder of glycosylation type 1a and congenital heart defects have already been reported, but ther...

Background & Aims:  Congenital heart disease (CHD) is the most common congenital anomaly, accounting for 28% of all congenital anomalies in infants. The present study was performed to determine the frequency, demographic characteristics, and clinical outcomes in neonates with CHD. Materials & Methods: This cross-sectional, descriptive-analytical study was conducted on 341 neonates with CHD adm...

The present study of 47 necropsy cases of congenital heart disease has revealed that cardiac defects occur as frequently in the African as in the non-African. The types of congenital heart disease and the associated non-cardiac malformations are similar to what has been described in non-Africans. Tetrad of Fallot was the commonest type of multiple defect and ventricular septal defect the most c...

Congenital heart defects are the most common malformations at birth. Due to the fact that the developmental windows at early stages close rapidly, the aim of this study was to determine the impact of congenital heart defects on the central nervous system at short and medium terms after applying traditional and quantitative electroencephalography techniques and a test of neurodevelopment. Twenty...

Introduction: Along with advances occurring in cardiopulmonary bypass (CPB) including improved anesthesia intubation and early surgical interventions, it has become possible to correct life-threatening congenital heart anatomic abnormalities in patients. Our study aimed to collect information from one of the most important centers of pediatric cardiac surgery in Iran since there is limited info...

Introduction: Hearing impairment is the most frequent sensorial congenital defect in newborns and has increased to 2–4 cases per 1,000 live births. Sensory-neural hearing loss (SNHL) accounts for more than 90% of all hearing loss. This disorder is associated with other congenital disorders such as renal, skeletal, ocular, and cardiac disorders. Given that congenital heart diseases are life-thre...

introduction: hearing impairment is the most frequent sensorial congenital defect in newborns and has increased to 2–4 cases per 1,000 live births. sensory-neural hearing loss (snhl) accounts for more than 90% of all hearing loss. this disorder is associated with other congenital disorders such as renal, skeletal, ocular, and cardiac disorders. given that congenital heart diseases are life-thre...