The main facial features of NS are hypertelorism (an abnormally increased distance between two organs or bodily parts, usually referring to an increased distance between the eyes), ptosis (a drooping or falling of the upper eyelid) and low-set rotated ears (Pic. 2) situated behind with a thickened helix (the prominent rim of the auricle). The cardiovascular defects most commonly associated with...

35 patients with unilateral sensorineural impairment and hearing levels within the normal range in the opposite ears were investigated by bilateral transtympanic electrocochleography (tiecog). only 19 patients (54%) satisfied the criteria for meniere's disease and 16 patients (46%) showed sensorineural impairment due to other etiologies. clinical studies have focused exclusively on the a m...