To discuss the clinical presentation, diagnosis, and treatment of hepatic venous outflow obstruction as a complication of polycystic liver disease, four cases diagnosed and treated at our institution have been reviewed and the information from six previously published case reports has been summarized. Eight of the 10 patients were women. All presented with severe ascites. Nine had polycystic ki...

Introduction: Budd-Chiari syndrome is a rare condition which can be defined as hepatic venous outflow obstruction occurring at any level between the small veins and junction of inferior vena cava right atrium. Symptoms may vary from mild or even asymptomatic for many years to fulminant failure. Imaging mainstay diagnosis BCS. Laboratory ematological tests are invaluable in recognizing hematolog...

The association of Budd-Chiari Syndrome (BCS) with coeliac disease has been understudied and underreported. Majority the cases this have reported from North Africa Southern Europe, due to a higher prevalence disease. BCS can present as acute, subacute, or chronic form is characterised by hepatic venous obstruction, either thrombotic non-thrombotic without any evidence sinusoidal obstruction syn...

Hepatic pseudolesions are defined as non-neoplastic focal abnormalities of the liver which can mimic or conceal true lesions. It is particularly common in due to its unique dual blood supply and existence multilevel anastomosis between them. Because recent advances CT MRI technology, they being increasingly encountered daily practice. Broadly be categorised (1) Focal parenchymal like fatty chan...

We report the cases of two renal transplant recipients suffering from idopathic portal hypertension, a condition characterised by increased portal venous pressure in the absence of both histological lesion of the liver and obstruction of the portal vein. In these two patients, perisnusoidal fibrosis, invisible by light microscopy, was demonstrated by electron microscopy; it is suggested that pa...

Budd-Chiari syndrome is an uncommon disorder characterized by the thrombotic or non-thrombotic obstruction of hepatic venous outflow anywhere along the venous course from the hepatic venules to the junction of the inferior vena cava and the right atrium. The etiology of Budd-Chiari syndrome is classified as primary, attributable to intrinsic intraluminal thrombosis or the development of venous ...

The Budd-Chiari syndrome is a heterogeneous group of disorders characterized by obstruction of hepatic venous outflow at any level from the small hepatic veins to the junction of the inferior vena cava with the right atrium. We present two cases of Budd- Chiari syndrome with severe ascites associated with polycythemia vera in first case and protein C deficiency in the second, in both cases tran...

Budd-Chiari syndrome is a rare but life-threatening disorder characterized by obstruction of the hepatic venous outflow. Treatment depends on underlying cause, extent of the obstruction and functional capacity of the liver. When all other therapy options are unsuccessful, liver transplant should be considered. Portal vein thrombosis (PVT) is a frequent event in patients with cirrhosis which can...