نتایج جستجو برای: hereditary spastic paraplegia

تعداد نتایج: 94252  

Journal: :Journal of medical genetics 2003
E Reid

The hereditary spastic paraplegias are a group of neurodegenerative conditions that all share the principal clinical feature of progressive lower limb spastic paralysis, caused by either failure of development or progressive degeneration of the corticospinal tract. The conditions are characterised by extreme genetic heterogeneity, with at least 20 genes involved. Until recently, no functional o...

Journal: :Bulletin of Problems Biology and Medicine 2019

Journal: :Brain & development 2010
Carlo Fusco Daniele Frattini Enrico Farnetti Davide Nicoli Bruno Casali Francesco Fiorentino Andrea Nuccitelli Elvio Della Giustina

Mutations in the SPG3A gene (atlastin protein) cause approximately 10% of autosomal-dominant hereditary spastic paraplegia. Most patients with an SPG3A mutation present with a pure phenotype and early-onset disease, although complicated forms with peripheral neuropathy are also reported. We report a new heterozygous S398F mutation in exon 12 of the SPG3A gene causing a very early-onset spastic ...

2017
Pedro J. Tomaselli Alexander M. Rossor Alejandro Horga Matilde Laura Julian C. Blake Henry Houlden Mary M. Reilly

Mutations in the kinesin family member 1A (KIF1A) gene have been associated with a wide range of phenotypes including recessive mutations causing hereditary sensory neuropathy and hereditary spastic paraplegia and de novo dominant mutations causing a more complex neurological disorder affecting both the central and peripheral nervous system. We identified by exome sequencing a de novo dominant ...

Journal: :Journal of neurology, neurosurgery, and psychiatry 1984
I D Young I F Pye J R Moore

An unusual form of hereditary spastic paraplegia is described. Affected females have a late-onset slowly progressive spastic paraparesis. Affected males show oligophrenia with a rapidly progressive spastic quadriplegia. The mode of inheritance is consistent with sex-linkage, with partial manifestation in female carriers.

Journal: :Annual Review of Neuroscience 2012

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید