A 9 year old boy with juvenile dermatomyositis developed pulmonary alveolar lipoproteinosis. This previously unreported association was treated successfully by bronchoalveolar lavage.

OBJECTIVE To identify risk factors associated with calcinosis in children and adolescents with juvenile dermatomyositis. METHODS A review was carried out of the medical records of 54 patients with juvenile dermatomyositis. Data were collected on demographic characteristics, clinical features: muscle strength (stages I to V of the Medical Research Council scale), pulmonary involvement (restric...

6. Rodero Prieto R, Camacho Lovillo MS, Lirola Cruz MJ. Generalized edema as a form of presentation of juvenile dermatomyositis. An Pediatr (Barc). 2013;79:271--2. 7. Zedan M, El-Ayouty M, Abdel-Hady H, Shouman B, El-Assmy M, Fouda A. Anasarca: Not a nephrotic syndrome but dermatomyositis. Eur J Pediatr. 2008;167:831--4. 8. Rafailidis PI, Kapaskelis A, Falagas ME. Periorbital and facial swellin...

Juvenile dermatomyositis is a systemic vasculopathy, affecting mainly the skin and muscle. In the United States, it is seen in more than three per million children per year. It is diagnosed on the basis of the criteria set by Bohan and Peter. The following review describes the characteristic clinical manifestations, the pathophysiology and immunology of the disease. The various treatment modali...

Juvenile dermatomyositis has variable clinical presentations both in and outside of pregnancy. A literature review indicated that optimal maternal and fetal outcomes can be anticipated when the pregnancy is undertaken while the disease is in remission. Poorer outcomes are associated with flare-up of the disease in early pregnancy compared with exacerbation in the second or third trimester, when...

Introduction Juvenile idiopathic arthritis (JIA) is a heterogeneous group of chronic arthritis that occurs in susceptible subjects and may be related to environmental triggers. In this regard, air pollution could be a potential contributor to autoimmune diseases onset and flare, as it has been recently reported by our group in juvenile systemic lupus erythematosus and dermatomyositis patients, ...