A 17 year old girl presented with asymptomatic linear depressed groove involving the midline of the forehead region which was progressively increasing over the past 1 year. The lesion was slowly extending to the scalp which became a major concern to the patient. There was no history of trauma preceding the development of the lesion. On examination, an ivory sclerotic depressed linear lesion mai...

We report the case of a young girl who presented with hemiparesis, seizures, and subtle features consistent with a linear form of facial morphea (en coup de sabre). She was treated with pulsed parenteral steroids and oral steroids and started on methotrexate. Magnetic resonance imaging results and neurologic problems improved after 6 months. Switching off inflammation early in the course of dis...

BACKGROUND Progressive Hemifacial Atrophy (PHA) is an acquired, typically unilateral, facial distortion with unknown etiology. The true incidence of this disorder has not been reported, but it is often regarded as a subtype of localized scleroderma. Historically, a debate existed whether PHA is a form of linear scleroderma, called morphea en coup de sabre (ECDS), or whether these conditions are...

BACKGROUND Localized scleroderma is characterized by a thickening of the skin from excessive collagen deposits. It is not a fatal disease, but quality of life can be adversely affected due to changes in skin appearance, joint contractures, and, rarely, serious deformities of the face and extremities. We present six cases of localized scleroderma in face from our surgical practice. METHODS We ...

© 2015 The Authors. doi: 10.2340/00015555-2100 Journal Compilation © 2015 Acta Dermato-Venereologica. ISSN 0001-5555 Localized scleroderma (LS) in childhood is a relatively rare fibrosing disorder of the skin and underlying tissues. Early subtle skin changes include hyperpigmented, hypopigmented, erythematous, or purplish patches. In particular, En coup de sabre (ECDS), a linear type of LS loca...