Definition of “functionally single ventricle” includes a wide spectrum of anatomical variants such as double inlet left or right ventricle, mitral or tricuspid atresia, unbalanced atrioventricular canal, heterotaxy syndrome with one normally developed ventricle or other congenital heart defects with severe hypoplasia of one of the ventricles [2]. Anatomical and hemodynamic abnormalities in thes...

introduction the eustachian valve (ev) remnant, when present in adults, is usually rudimentary. however, in echocardiographic examinations, it may appear as a mobile long structure in the right atrium, and it rarely protrudes into the right ventricle. when it is quite large, the ev remnant could be misdiagnosed as a right atrial tumor, thrombus, or vegetation. case presentation an 83-year-old p...

In the present case report, we describe a malformation consisting of a double-outlet right ventricle with an intact ventricular septum diagnosed in a 3-day-old female newborn. To our knowledge 35 cases have been described in the literature. The diagnosis was made by two-dimensional echocardiography and confirmed by angiocardiography. An inadequate opening in the interatrial septum and hypoplasi...

OBJECTIVE One-and-a-half ventricle repair is a surgical option for complex cardiac anomalies characterized by right-ventricle hypoplasia or dysfunction. The long-term result analyses or large clinical reviews are rare. The aim of this study is to evaluate the long-term functional results of this surgical procedure. METHODS The 29 patients, who underwent one-and-a-half ventricle repair from Ju...

OBJECTIVE Management of pulmonary atresia with intact ventricular septum (PAIVS) can be directed to either biventricular repair or univentricular palliation. The optimal management strategy has yet to be defined. METHODS All patients operated at the Royal Children's Hospital, Melbourne for PAIVS between 1990 and 2006 (n = 81) were reviewed. Patients were retrospectively stratified into a simp...

A case of congenital diverticulum of the left ventricle associated with a ventricular septal defect and severe hypoplasia of the right ventricle without tricuspid or pulmonary atresia is described and the relevant literature is reviewed. The distinction between true muscular diverticulae and congenital apical aneurysms is made, the latter term being preferred for similar abnormalities described...

A 9-day-old neonate weighing 3 kg was referred to our institution for cyanosis and a systolic murmur. A 2-dimensional echocardiogram suggested SDL, levocardia, criss-cross heart with double-outlet right ventricle, hypoplasia of the tricuspid valve and right ventricle, and severe pulmonary stenosis. A real-time 3-dimensional echocardiogram (Sonos 7500, Philips Medical Systems, Andover, Mass) dem...

BACKGROUND Double chambered right ventricle (DCRV) is a congenital heart anomaly where the right ventricle is divided into two chambers. We describe, for the first time, an unusual combination of DCRV combined with some other congenital heart defects. CASE PRESENTATION A 1.2-year-old Golden Retriever was presented with lethargy, exercise intolerance and ascites. Physical examination revealed ...

[1] Morell VO, Wearden PD. Aortic translocation for the management of transposition of the great arteries with a ventricular septal defect, pulmonary stenosis, and hypoplasia of the right ventricle. Eur J Cardiothorac Surg 2007;31:552—4. [2] Sayin OA, Ugurlucan M, Saltik L, Sungur Z, Tireli E. Modified Nikaidoh procedure for transposition of great arteries, ventricular septal defect and left ve...