left ventricular non-compaction cardiomyopathy is a rare congenital cardiomyopathy that affects both children and adults. since the clinical manifestations are not sufficient to establish diagnosis, echocardiography is the diagnostic tool that makes it possible to document ventricular non-compaction and establish prognostic factors. we report a 47-year-old woman with a history of dilated cardio...

a 76-yr-old man with unipolar ventricular pacemaker, previously implanted in the right ventricular apex, presented with syncopal attack and twitching of the right pectoralis muscle. he finally was diagnosed as having twiddler's syndrome. the patient had a pulse rate of 36/min and cannon waves in the neck veins. chest radiography showed a dislodged pacing lead completely wrapped around the pulse...

this paper presents the case of a 35 year-old woman with symptoms of heart failure from the last month. a physical examination at admission showed paleness, dyspnea, peripheral edema and fatigue. in a two-dimensional echocardiography and transesophageal echocardiography, normal thickness but severe left and right ventricular dysfunction with severe pericardial effusion and thickened pericardium...

we assessed different systolic cardiac indices to detect left and right ventricular systolic dysfunction in cirrhotic patients before liver transplantation. between 2010-2011, 81 consecutive individuals with confirmed hepatic cirrhosis who were a candidate for liver transplantation were enrolled in this study. a total of 32 age and sex matched healthy volunteers were also selected as the contro...

Introduction: Arterial tortuosity syndrome (ATS), an autosomal recessive rare connective tissue disorder characterized by tortuosity, elongation and stenosis in the large and medium sized arteries. It manifestations include vascular and nonvascular connective tissue related symptoms. In this literature we describe the first cases of ATS from Iran. Case report: A six-months-old female wa...

Background: Assessment of myocardial function is essential in heart disease, but in regard to systolic and diastolic functions such evaluation has limitation. Ejection fraction is difficult to assess in abnormally-shaped ventricles, and diastolic inflow velocity pattern may be fused because of tachycardia. Objective: A myocardial performance index (MPI) or Tei index has been developed for adult...

an elevated pulmonary artery pressure (pap) from any cause is associated with increased mortality, especially in cases of primary pulmonary arterial hypertension (pah). one of the many reasons behind a bad prognosis is the inherent difficulty in assessing right ventricular (rv) function with reproducible methods. intensive research involving the left heart has made it relatively easy to assess ...