نتایج جستجو برای: s thrombasthenia

تعداد نتایج: 711432  

Journal: :Blood 1988
P F Nievelstein J J Sixma

Previous studies have indicated that activated blood platelets interact with fibronectin through binding of fibronectin to the glycoprotein IIb-IIIa complex (GPIIb-IIIa). The cell attachment site of fibronectin with its crucial arg-gly-asp(-ser) [RGD(S)]sequence is involved in these bindings. We studied the importance of these interactions for the fibronectin dependence of platelet adhesion und...

Journal: :Blood 1990
P F Bray M A Shuman

The platelet fibrinogen receptor, which is composed of glycoproteins IIb (GPIIb) and IIIa (GPIIIa), belongs to a large family of receptors that participate in a multitude of biologically important adhesive interactions. Platelets from most patients with the autosomal recessive bleeding disorder, Glanzmann's thrombasthenia, are deficient in GPIIb and GPIIIa. We have used cDNA probes to analyze t...

Journal: :Proceedings of the Royal Society of Medicine 1970

Journal: :Journal of Clinical Pathology 1968

Journal: :Journal of Clinical Case Reports 2012

Journal: :Journal of obstetrics and gynaecology of India 2014
Chandrakala Magudapathi Suthanthira Kannan

Glanzmann’s thrombasthenia is a rare autosomal recessive hemorrhagic disorder caused by abnormal platelet glycoprotein complex (GP IIb-IIIa) presenting with hemorrhagic symptoms. Pregnancy is not uncommon because fertility is not affected but an association is rare. Also delivery often results in haemorrhage. Newborn thrombocytopenia is occasionally severe, but is always transitory. We report a...

Journal: :Haematologica 2015
Man-Chiu Poon Roseline d'Oiron Rainer B Zotz Niels Bindslev Matteo Nicola Dario Di Minno Giovanni Di Minno

Standard treatment for Glanzmann thrombasthenia, a severe inherited bleeding disorder, is platelet transfusion. Recombinant factor VIIa is reported to be effective in Glanzmann thrombasthenia with platelet antibodies and/or refractoriness to platelet transfusions. We aimed to evaluate recombinant factor VIIa effectiveness and safety for the treatment and prevention of surgical bleeding in patie...

Journal: :British journal of haematology 2002
Isabelle Martin Fayçal Kriaa Valérie Proulle Benoît Guillet Cécile Kaplan Roseline D'Oiron Marianne Debré Edith Fressinaud Yyes Laurian Gil Tchernia Bernard Charpentier Thierry Lambert Marie Dreyfus

Type I Glanzmann's thrombasthenia is a rare congenital platelet function disorder, characterized by undetectable platelet membrane glycoprotein IIb-IIIa (GPIIb-IIIa). Severe bleeding is controlled by transfusion of normal platelets, leading in some cases to the occurrence of anti-GPIIb-IIIa isoantibodies, which induces a loss of transfused platelet efficacy. We used immunoadsorption on protein ...

2002
O. Shpilberg I. Rabi R. Walden D. Harats K. S. Tyrrell B. Coller U. Seligsohn

Background—Platelets have been suggested to play a role in the early development of atherosclerosis. As one test of this hypothesis, we assessed whether patients with Glanzmann thrombasthenia who lack platelet glycoprotein IIb 3 (GPIIb/IIIa) complexes or both IIb 3 and the more ubiquitous v 3 cell membrane complexes are protected from development of atherosclerosis. Methods and Results—Seven pa...

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