Introduction: Literature regarding the different degrees of hearing loss in patients with Cornelia de Lange syndrome (CDLS) reports that half of the affected patients exhibit severe to profound sensorineural hearing loss. We present the first pre-school child with CDLS who underwent cochlear implantation for congenital profound sensorineural hearing loss.   Case Report: A 3-year-old boy with CD...

Background: Hearing loss due to chronic otitis media is common. The purpose of this study was to evaluate hearing before and after canal wall up, canal wall down mastoidectomy and tympanoplasty. Methods: From 2004 to 2007, all patients with chronic otitis media who were admitted at the Department of Otolaryngology, Babol Medical University were studied. For 126 patients' canal wall up, canal wa...

inner ear cells are sensitive to some metabolic and hormonal disorders, but the relation between chronic renal failure (crf), regular dialysis treatment (rdt) and sensorineural hearing loss (snhl) is still a debatable field. the object of this paper was to verify the presence of snhl in patients submitted to hemodialysis with different duration due to crf and in those submitted to conservative ...

Introduction: Children learn to communicate by hearing sounds. If there is hearing loss, the cognitive and speaking abilities and language learning will deteriorate. Early detection and intervention are important factors in the successful treatment of hearing loss in children. Hearing loss (HL) is divided into two main groups: conductive hearing loss (CHL) and sensorineural hearing loss (SNHL)...

OBJECTIVE To investigate the cerebral gray matter volume alterations in unilateral sudden sensorineural hearing loss patients within the acute period by the voxel-based morphometry method, and to determine if hearing impairment is associated with regional gray matter alterations in unilateral sudden sensorineural hearing loss patients. STUDY DESIGN Prospective case study. SETTING Tertiary c...

Advances in sequencing technologies and increased understanding of the contribution of genetics to congenital sensorineural hearing loss have led to vastly improved outcomes for patients and their families. Next-generation sequencing and diagnostic panels have become increasingly reliable and less expensive for clinical use. Despite these developments, the diagnosis of genetic sensorineural hea...

loss of hearing is a known problem in patients with chronic renal failure, occurring in 40-xo% of cases and being most often of the high frequency sensorineural type. we performed a study on 50 patients with this disease, including 20 who had undergone a successful kidney transplantation. our results show an 80% incidence of hearing loss in these patients and a chance of improvement in at least...

objective: mumps infection is endemic in iran and mumps parotiditis is a common disease in iranian children. there has been a dramatic decrease in the worldwide incidence of mumps since the introduction and use in 1968 of the very effective and inexpensive mumps vaccine. in iran probably due to a higher percentage of unvaccinated young persons material& methods: this descriptive case-series stu...

conclusion we concluded that cmv is the most common cause of intrauterine infection in infants aged less than 6 months as compared to the healthy ones. we prefer, at least in our country, to consider seropositive (cmv-igm) infants suspected of intrauterine infection (less than 6 months) as congenital form. to arrest the natural progression of congenital cmv, we recommend prolonged course of ora...

Introduction: Sudden sensorineural hearing loss (SSNHL) has a prevalence of 10 in 100,000. Viral infections, vascular obstruction and rupture of the intracochlear membranes are supposed to be its most common etiologies. About 40% of patients experience vertigo or imbalance. The VEMP (vestibular evoked myogenic potentials) test is a known approach for detailed study of the labyrinth. The advant...